Hypersplenism Associated With Late-Presenting Congenital Diaphragmatic Hernia: A Rare Combination. Case Report

被引：4

作者：

Lu, Xue-Xin ^{[1
]}

Shen, Zhen ^{[1
]}

Dong, Kui-Ran ^{[1
]}

Zheng, Shan ^{[1
]}

机构：

[1] Fudan Univ, Dept Pediat Surg, Childrens Hosp, 399 Wanyuan Rd, Shanghai 201102, Peoples R China

来源：

MEDICINE | 2016年 / 95卷 / 21期

关键词：

D O I：

10.1097/MD.0000000000003707

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Congenital diaphragmatic hernia (CDH) is a rare developmental anomaly of the diaphragm that mainly presents mainly in newborns. Even less common is late-onset CDH associated with hypersplenism. We report a 10-year-old male who presented with coughing, blood-stained sputum, and fever. He was diagnosed with CDH complicating hypersplenism after computed tomography was done. The patient was treated by CDH repair and splenectomy, and remained asymptomatic at 6-month follow-up. Computed tomography can be an important diagnostic option in this rare combination of CDH and hypersplenism, and surgical intervention is strongly recommended.

引用

页数：4

共 12 条

[1] Late-presenting congenital diaphragmatic hernia in children: a clinical spectrum [J].

Baglaj, M .

PEDIATRIC SURGERY INTERNATIONAL, 2004, 20 (09) :658-669

[2] Big spleens and hypersplenism: fix it or forget it? [J].

Boyer, Thomas D. ;

Habib, Shahid .

LIVER INTERNATIONAL, 2015, 35 (05) :1492-1498

[3]

BUTLER N, 1962, LANCET, V1, P659

[4] Late-presenting congenital diaphragmatic hernia in childhood [J].

Chao, Pei-Hsin ;

Chuang, Jiin-Haur ;

Lee, Shin-Yi ;

Huang, Hsin-Chun .

ACTA PAEDIATRICA, 2011, 100 (03) :425-428

[5] Review of guidelines for the prevention and treatment of infection in patients with an absent or dysfunctional spleen: Prepared on behalf of the British Committee for Standards in Haematology by a Working Party of the Haemato-Oncology Task Force [J].

Davies, John M. ;

Lewis, Michael P. N. ;

Wimperis, Jennie ;

Rafi, Imran ;

Ladhani, Shamez ;

Bolton-Maggs, Paula H. B. .

BRITISH JOURNAL OF HAEMATOLOGY, 2011, 155 (03) :308-317

[6] Rare Case Report - Congenital Diaphragmatic Hernia Presentation in Adult [J].

Gujar, Ajay ;

Rodrigues, Dale Don ;

Patil, Kundan ;

Tambe, Uday ;

Sinha, Shubha ;

Bhushan, Abhishek .

INDIAN JOURNAL OF SURGERY, 2013, 75 :S44-S46

[7] Portal hypertension and hypersplenism in a patient with a Bochdalek hernia: a case report [J].

Kennedy, R. ;

Donaghy, A. ;

Ahmad, J. ;

McManus, K. ;

Clements, W. D. B. .

IRISH JOURNAL OF MEDICAL SCIENCE, 2009, 178 (01) :111-113

[8] Congenital diaphragmatic hernia [J].

Leeuwen, Lisette ;

Fitzgerald, Dominic A. .

JOURNAL OF PAEDIATRICS AND CHILD HEALTH, 2014, 50 (09) :667-673

[9] Epidemiology of congenital diaphragmatic hernia in Europe: a register-based study [J].

McGivern, Mark R. ;

Best, Kate E. ;

Rankin, Judith ;

Wellesley, Diana ;

Greenlees, Ruth ;

Addor, Marie-Claude ;

Arriola, Larraitz ;

de Walle, Hermien ;

Barisic, Ingeborg ;

Beres, Judit ;

Bianchi, Fabrizio ;

Calzolari, Elisa ;

Doray, Berenice ;

Draper, Elizabeth S. ;

Garne, Ester ;

Gatt, Miriam ;

Haeusler, Martin ;

Khoshnood, Babak ;

Klungsoyr, Kari ;

Latos-Bielenska, Anna ;

O'Mahony, Mary ;

Braz, Paula ;

McDonnell, Bob ;

Mullaney, Carmel ;

Nelen, Vera ;

Queisser-Luft, Anette ;

Randrianaivo, Hanitra ;

Rissmann, Anke ;

Rounding, Catherine ;

Sipek, Antonin ;

Thompson, Rosie ;

Tucker, David ;

Wertelecki, Wladimir ;

Martos, Carmen .

ARCHIVES OF DISEASE IN CHILDHOOD-FETAL AND NEONATAL EDITION, 2015, 100 (02) :F137-F144

[10] Bochdalek diaphragmatic hernia: not only a neonatal disease [J].

Mei-Zahav, M ;

Solomon, M ;

Trachsel, D ;

Langer, JC .

ARCHIVES OF DISEASE IN CHILDHOOD, 2003, 88 (06) :532-535

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