Association of Klinefelter syndrome and abdominal teratoma: A case report

被引:8
作者
Czauderna, P
Stoba, C
Wysocka, B
Iliszko, M
机构
[1] Med Univ Gdansk, Dept Pediat Surg, Clin Pediat Surg, PL-80803 Gdansk, Poland
[2] Med Univ Gdansk, Dept Biol & Genet, PL-80803 Gdansk, Poland
关键词
Klinefelter syndrome; teratoma; germ cell tumors;
D O I
10.1016/S0022-3468(98)90217-2
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Extragonadal germ cell tumors are rare. The association with Klinefelter syndrome has become observed recently. A case of an Ii-month-old infant with Klinefelter syndrome and a retroperitoneal mature teratoma is presented. In the tumor and lymphocytes, a 47,XXY karyotype was found. The association of Klinefelter syndrome with germ cell tumors and its possible explanations are discussed. Copyright (C) 1998 by W.B. Saunders Company.
引用
收藏
页码:774 / 775
页数:2
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