Beckwith-Wiedemann syndrome and virilizing cortical adrenal tumor in a child

被引：9
作者：
Sbragia-Neto, L
Melo, AA
Guerra, G
Marini, SHVD
Baptista, MTM
de Matos, PS
de Oliveira, AG
Bustorff-Silva, JM
机构：
[1] State Univ Campinas, Fac Med Sci, Dept Pathol, Sao Paulo, Brazil
[2] State Univ Campinas, Fac Med Sci, Div Pediat Surg, Sao Paulo, Brazil
[3] State Univ Campinas, Fac Med Sci, Div Pediat Endocrinol, Sao Paulo, Brazil
来源：
JOURNAL OF PEDIATRIC SURGERY | 2000年 / 35卷 / 08期
关键词：
Beckwith-Wiedemann syndrome; adrenal gland diseases; adrenal; omphalocele;
D O I：
10.1053/jpsu.2000.8771
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
The authors report a case of a virilizing adrenal tumor that developed in a 2-year-old child with Beckwith-Wiedemann syndrome (BWS), He had a fetal diagnosis of omphalocele and a history of neonatal adrenal cysts. The importance of prenatal diagnosis of BWS and postnatal follow-up of tumors is discussed. The differential diagnosis of adrenal pathologies occurring in BWS also is reviewed. J Pediatr Surg 35:1269-1277. Copyright (C) 2000 by W.B. Saunders Company.
引用
收藏
页码：1269 / 1271
页数：3
相关论文
共 22 条
  • [1] Bilateral multiple adrenal pseudocysts associated with incomplete Beckwith-Wiedemann syndrome
    Ciftci, AO
    Salman, AB
    Tanyel, FC
    Hicsonmez, A
    [J]. JOURNAL OF PEDIATRIC SURGERY, 1997, 32 (09) : 1388 - 1390
  • [2] VIRILIZING ADRENAL ADENOMA IN AN ADULT WITH THE BECKWITH-WIEDEMANN SYNDROME - PARADOXICAL RESPONSE TO DEXAMETHASONE
    CLOUSTON, WM
    CANNELL, GC
    FRYAR, BG
    SEARLE, JW
    MARTIN, NI
    MORTIMER, RH
    [J]. CLINICAL ENDOCRINOLOGY, 1989, 31 (04) : 467 - 473
  • [3] WIEDEMANN-BECKWITH SYNDROME
    ENGSTROM, W
    LINDHAM, S
    SCHOFIELD, P
    [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1988, 147 (05) : 450 - 457
  • [4] ADRENOCORTICAL NEOPLASMS WITH HEMIHYPERTROPHY BRAIN TUMORS AND OTHER DISORDERS
    FRAUMENI, JF
    MILLER, RW
    [J]. JOURNAL OF PEDIATRICS, 1967, 70 (01) : 129 - +
  • [5] ADRENOCORTICAL CARCINOMA AND CONGENITAL HEMIHYPERTROPHY
    HAICKEN, BN
    SCHULMAN, NH
    SCHNEIDER, KM
    [J]. JOURNAL OF PEDIATRICS, 1973, 83 (02) : 284 - 285
  • [6] ADRENAL CALCIFICATION IN BECKWITH-WIEDEMANN SYNDROME
    ICHIBA, Y
    AOYAMA, K
    [J]. AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1977, 131 (11): : 1296 - 1297
  • [7] ADRENAL HEMORRHAGE IN NEONATES - REPORT OF 5 CASES AND REVIEW OF THE LITERATURE
    KHURI, FJ
    ALTON, DJ
    HARDY, BE
    COOK, GT
    CHURCHILL, BM
    [J]. JOURNAL OF UROLOGY, 1980, 124 (05) : 684 - 687
  • [8] BENIGN HEMORRHAGIC ADRENOCORTICAL MACROCYSTS IN BECKWITH-WIEDEMANN SYNDROME
    MCCAULEY, RGK
    BECKWITH, JB
    ELIAS, ER
    FAERBER, EN
    PREWITT, LH
    BERDON, WE
    [J]. AMERICAN JOURNAL OF ROENTGENOLOGY, 1991, 157 (03) : 549 - 552
  • [9] NEBLETT WW, 1987, AM SURGEON, V53, P117
  • [10] PRENATAL-DIAGNOSIS OF BILATERAL ADRENAL CYSTS
    PATTI, G
    FIOCCA, G
    LATINI, T
    CELLI, E
    BELLUSSI, A
    NAZZICONE, P
    [J]. JOURNAL OF UROLOGY, 1993, 150 (04) : 1189 - 1191
123