Parry Romberg syndrome and linear scleroderma in coup de sabre mimicking Rasmussen encephalitis

被引：38
作者：
Carreno, M. [1 ]
Donaire, A.
Barcelo, M. I.
Rumia, J.
Falip, M.
Agudo, R.
Bargallo, N.
Setoain, X.
Boget, T.
Raspall, A.
Pintor, L.
Ribalta, T.
机构：
[1] Hosp Clin Barcelona, Dept Neurol, Barcelona, Spain
[2] Hosp Clin Barcelona, Dept Pathol, Barcelona, Spain
[3] Hosp Clin Barcelona, Dept Neurosurg, Barcelona, Spain
[4] Hosp Clin Barcelona, Dept Radiol, Barcelona, Spain
[5] Hosp Clin Barcelona, Dept Nucl Med, Barcelona, Spain
[6] Hosp Clin Barcelona, Dept Neuropsychol, Barcelona, Spain
[7] Hosp Clin Barcelona, Dept Psychiat, Barcelona, Spain
[8] Hosp Son Dureta, Dept Neurol, Palma de Mallorca, Spain
来源：
NEUROLOGY | 2007年 / 68卷 / 16期
关键词：
D O I：
10.1212/01.wnl.0000259523.09001.7a
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
We present one patient with Parry Romberg syndrome and another with linear scleroderma in coup de sabre, with focal neurologic deficits and intractable seizures arising from the hemisphere ipsilateral to the cutaneous lesion. Brain MRI showed progressive hemispheric atrophy. Pathology after functional hemispherectomy showed chronic inflammatory features suggestive of Rasmussen encephalitis.
引用
收藏
页码：1308 / 1310
页数：3
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