Primary hypertrophic osteoarthropathy: ultrasound and MRI findings

被引：6

作者：

Adams, Brook ^{[1
,2
]}

Amin, Tania ^{[2
,3
]}

Leone, Valentina ^{[2
,3
]}

Wood, Mark ^{[2
,3
]}

Kraft, Jeannette K. ^{[1
,2
]}

机构：

[1] Leeds Childrens Hosp, Clarendon Wing Radiol Dept, Leeds LS2 9NS, W Yorkshire, England

[2] Leeds Gen Infirm, Leeds LS2 9NS, W Yorkshire, England

[3] Leeds Childrens Hosp, Dept Paediat Rheumatol, Leeds LS2 9NS, W Yorkshire, England

来源：

PEDIATRIC RADIOLOGY | 2016年 / 46卷 / 05期

关键词：

Child; Magnetic resonance imaging; Pachydermoperiostosis; Periostitis; Primary hypertrophic osteoarthropathy; Ultrasound; PACHYDERMOPERIOSTOSIS; MUTATIONS;

D O I：

10.1007/s00247-016-3544-8

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Primary hypertrophic osteoarthropathy is a rare genetic disorder related to failures in prostaglandin metabolism. Patients present with joint pain, limb enlargement, skin thickening and finger clubbing. Radiographs show characteristic periosteal reaction and thickening along the long bones. We present MRI and US findings in a child with the condition. Ultrasound showed echogenic tissue surrounding the long bones, presumably reflecting oedema and inflammatory tissue. Doppler sonograms demonstrated increased vascularity on the surface of some superficial bony structures.

引用

页码：727 / 730

页数：4

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