Vasculitis and long standing ankylosing spondylitis in a patient with familial Mediterranean fever

被引:0
作者
Taylan, Ali [1 ]
Yildiz, Yasar [2 ]
Sari, Ismail [2 ]
Ozkok, Guliz [3 ]
机构
[1] Izmir Tepecik Teaching & Res Hosp, Dept Rheumatol, Izmir, Turkey
[2] Izmir BozyakaTraining & Res Hosp, Dept Internal Med, Izmir, Turkey
[3] Izmir BozyakaTraining & Res Hosp, Dept Pathol, Izmir, Turkey
来源
Journal of Research in Medical Sciences | 2014年 / 19卷 / 10期
关键词
Ankylosing spondylitis; familial Mediterranean fever; leukocytoklastic vasculitis; vasculitis; CUTANEOUS VASCULITIS; IGA;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Coexistence of familial Mediterranean fever (FMF) and other inflammatory disorders has been frequently reported, but no specific underlying factor has been identified. We report a patient with FMF who is presented with long-standing ankylosing spondylitis (AS) and cutaneous leukocytoklastic vasculitis (LV) of the lower limbs. It is the first report on combination of FMF with AS and LV. The Mediterranean Fever (MEFV) gene mutation of heterozygote (R202Q/R726A) and HLA-B27 are detected in this case, and are believed to form genetic susceptibility to LV.
引用
收藏
页码:1009 / 1011
页数:3
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