Late Presentation of Congenital Diaphragmatic Hernia in Patients With Cystic Fibrosis

被引：1
作者：
Goetz, Danielle M. [1 ]
Burns, Cortland [2 ]
Segura, Bradley J. [2 ]
Weiner, Daniel J. [1 ]
机构：
[1] Childrens Hosp Pittsburgh, Div Pulm Med, Dept Pediat, Pittsburgh, PA 15201 USA
[2] Childrens Hosp Pittsburgh, Dept Pediat Surg, Pittsburgh, PA 15201 USA
来源：
PEDIATRIC PULMONOLOGY | 2010年 / 45卷 / 04期
关键词：
cystic fibrosis; congenital diaphragmatic hernia; late presentation of congenital diaphragmatic hernia; lung function; pulmonary function; PULMONARY-FUNCTION; SURVIVORS; MORBIDITY; INFANTS;
D O I：
10.1002/ppul.21173
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Late presentation of congenital diaphragmatic hernia (CDH) is unusual, especially in patients with cystic fibrosis (CF). To our knowledge, cases of CDH in CF patients and the combined effects on lung function have not been previously described. Here we report two cases of late presenting CDH in CF patients and describe effects on lung function. Late presentation of CDH in CF patients can cause gastrointestinal or respiratory symptoms and requires a high index of suspicion as well as proper interpretation of imaging. In patients with CF and CDH, lung function abnormalities could include obstructive, restrictive defects, or combined defects. Pediatr Pulmonol. 2010; 45:403-405. (C) 2010 Wiley-Liss, Inc.
引用
收藏
页码：403 / 405
页数：3
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