Introduction

被引：3

作者：

Bendotti, Caterina ^{[1
]}

Bonetto, Valentina ^{[2
]}

Migheli, Antonio ^{[3
]}

机构：

[1] IRCCS Ist Ric Farmacol Mario Negri, Dept Neurosci, Mol Neurobiol Lab, Milan, Italy

[2] IRCCS Ist Ric Farmacol Mario Negri, Dept Mol Biochem & Pharmacol, Lab Translat Prote, Milan, Italy

[3] Ctr Reg Diag & Osservaz Malattie Prioniche DOMP A, Turin, Italy

来源：

BRAIN PATHOLOGY | 2016年 / 26卷 / 02期

关键词：

AMYOTROPHIC-LATERAL-SCLEROSIS; MOUSE MODELS; ALS; MECHANISMS; VARIABILITY; CELLS;

D O I：

10.1111/bpa.12349

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：224 / 226

页数：3

共 20 条

[1]

Appel S H, 2011, Acta Myol, V30, P4

[2] Lessons from models of SOD1-linked familial ALS [J].

Bendotti, C ;

Carrì, MT .

TRENDS IN MOLECULAR MEDICINE, 2004, 10 (08) :393-400

[3] Poly-dipeptides encoded by the C9orf72 repeats bind nucleoli, impede RNA biogenesis, and kill cells [J].

Kwon, Ilmin ;

Xiang, Siheng ;

Kato, Masato ;

Wu, Leeju ;

Theodoropoulos, Pano ;

Wang, Tao ;

Kim, Jiwoong ;

Yun, Jonghyun ;

Xie, Yang ;

McKnight, Steven L. .

SCIENCE, 2014, 345 (6201) :1139-1145

[4] Defining the genetic connection linking amyotrophic lateral sclerosis (ALS) with frontotemporal dementia (FTD) [J].

Lattante, Serena ;

Ciura, Sorana ;

Rouleau, Guy A. ;

Kabashi, Edor .

TRENDS IN GENETICS, 2015, 31 (05) :263-273

[5] The Role of Skeletal Muscle in Amyotrophic Lateral Sclerosis [J].

Loeffler, Jean-Philippe ;

Picchiarelli, Gina ;

Dupuis, Luc ;

De Aguilar, Jose-Luis Gonzalez .

BRAIN PATHOLOGY, 2016, 26 (02) :227-236

[6] The neuropathology associated with repeat expansions in the C9ORF72 gene [J].

Mackenzie, Ian R. A. ;

Frick, Petra ;

Neumann, Manuela .

ACTA NEUROPATHOLOGICA, 2014, 127 (03) :347-357

[7] Differences in protein quality control correlate with phenotype variability in 2 mouse models of familial amyotrophic lateral sclerosis [J].

Marino, Marianna ;

Papa, Simonetta ;

Crippa, Valeria ;

Nardo, Giovanni ;

Peviani, Marco ;

Cheroni, Cristina ;

Trolese, Maria Chiara ;

Lauranzano, Eliana ;

Bonetto, Valentina ;

Poletti, Angelo ;

DeBiasi, Silvia ;

Ferraiuolo, Laura ;

Shaw, Pamela J. ;

Bendotti, Caterina .

NEUROBIOLOGY OF AGING, 2015, 36 (01) :492-504

[8] Rodent models of amyotrophic lateral sclerosis [J].

McGoldrick, Philip ;

Joyce, Peter I. ;

Fisher, Elizabeth M. C. ;

Greensmith, Linda .

BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, 2013, 1832 (09) :1421-1436

[9] New In Vitro Models to Study Amyotrophic Lateral Sclerosis [J].

Myszczynska, Monika ;

Ferraiuolo, Laura .

BRAIN PATHOLOGY, 2016, 26 (02) :258-265

[10] New Insights on the Mechanisms of Disease Course Variability in ALS from Mutant SOD1 Mouse Models [J].

Nardo, Giovanni ;

Trolese, Maria Chiara ;

Tortarolo, Massimo ;

Vallarola, Antonio ;

Freschi, Mattia ;

Pasetto, Laura ;

Bonetto, Valentina ;

Bendotti, Caterina .

BRAIN PATHOLOGY, 2016, 26 (02) :237-247

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