Successful Treatment of Protein-Losing Enteropathy and Plastic Bronchitis by Biphasic Cuirass Ventilation in a Patient with Failing Fontan Circulation

被引：7

作者：

Okada, Seigo ^{[1
]}

Muneuchi, Jun ^{[1
]}

Nagatomo, Yusaku ^{[1
]}

Nonaka, Kaori ^{[2
]}

Iida, Chiaki ^{[1
]}

Shirouzu, Hiromitsu ^{[1
]}

Matsuoka, Ryohei ^{[1
]}

Watanabe, Mamie ^{[1
]}

Joo, Kunitaka ^{[1
]}

机构：

[1] Kyushu Hosp, Japan Community Healthcare Org, Dept Pediat, Fukuoka, Fukuoka, Japan

[2] Kyushu Hosp, Japan Community Healthcare Org, Dept Rehabil, Fukuoka, Fukuoka, Japan

来源：

INTERNATIONAL HEART JOURNAL | 2018年 / 59卷 / 04期

关键词：

Central venous pressure; Congenital heart disease; Continuous negative extrathoracic pressure; Functionally univentricular circulation; Low cardiac output; MANAGEMENT; PRESSURE; FAILURE;

D O I：

10.1536/ihj.17-292

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We present a 16-year-old male patient with hypoplastic left heart syndrome who developed protein-losing enteropathy (PLE) and plastic bronchitis (PB) after a Fontan operation. He received medical therapies, including albumin infusion. unfractionated heparin, and high-dose anti-aldosterone therapy but could not obtain clinical relief. Biphasic cuirass ventilation (BCV) led to expectoration of bronchial casts and prompt resolution of PB. Notably, clinical symptoms related to PLE were dramatically improved after center dot starting BCV. A brief period of BCV increased stroke volume from 26 +/- 1.4 to 39 +/- 4.0 mL. This case suggests that BCV could be an effective treatment for PLE in patients with failing Fontan circulation.

引用

页码：873 / 876

页数：4

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