Pulmonary capillary hemangiomatosis: Radiographic appearance

被引:33
作者
Lippert, JL [1 ]
White, CS [1 ]
Cameron, EW [1 ]
Sun, CC [1 ]
Liang, XY [1 ]
Rubin, LJ [1 ]
机构
[1] Univ Maryland, Med Syst, Dept Radiol, Baltimore, MD 21201 USA
关键词
pulmonary hypertension; capillary hemangiomatosis; lung hemorrhage;
D O I
10.1097/00005382-199801000-00012
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Pulmonary capillary hemangiomatosis is a rare disorder that is characterized pathologically by formation of capillaries along alveolar walls that may ultimately invade the pulmonary parenchyma and pulmonary arteries. The clinic presentation overlaps that of primary pulmonary hypertension, but the natural history of pulmonary capillary hemangiomatosis is one of rapid deterioration. The typical radiographic appearance is a diffuse bilateral reticulonodular pattern associated with enlarged central pulmonary arteries.
引用
收藏
页码:49 / 51
页数:3
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