Interruption of the inferior vena cava with azygos termination associated with congenital absence of portal vein

被引:21
作者
Le Borgne, T
Paineau, J
Hamy, A
Dupas, B
Lerat, F
Raoul, S
Hamel, A
Robert, R
Armstrong, O
Rogez, JM
机构
[1] Fac Med Nantes, Lab Anat, F-44035 Nantes, France
[2] CHU Nantes, Hop GR Laennec, Serv Chirurg Gen & Digest, F-44800 St Herblain, France
[3] CHU Nantes, Hotel Dieu, Serv Radiol, F-44093 Nantes, France
关键词
inferior vena cava; azygos continuation; portal vein; congenital anomalies;
D O I
10.1007/s00276-000-0197-x
中图分类号
R602 [外科病理学、解剖学]; R32 [人体形态学];
学科分类号
100101 ;
摘要
The authors report an exceptional and well-documented case of interruption of the retrohepatic segment of the inferior vena cava with an "azygos continuation", combined with absence of the portal vein. The only known combination of congenital anomalies of the inferior vena cava and the portal vein was that of an "azygos continuation" and a preduodenal portal vein. The double interruption, portal and inferior caval, may be associated with a disturbance of preferential flows induced by the left umbilical thrust. According to hemodynamic theory, the left umbilical flow is the determining factor in organogenesis of the portal vein and the retrohepatic segment of the inferior vena cava.
引用
收藏
页码:197 / 202
页数:6
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