Evans Syndrome in a Jehovah's Witness

被引：0

作者：

Leonhardt, Lex P. ^{[1
]}

Pervez, Aamir ^{[1
]}

Calvo, Alejandro ^{[2
]}

机构：

[1] Kettering Med Ctr, Internal Med, Dayton, OH 45429 USA

[2] Kettering Med Ctr, Hematol & Med Oncol, Dayton, OH USA

来源：

CUREUS JOURNAL OF MEDICAL SCIENCE | 2021年 / 13卷 / 06期

关键词：

idiopathic thrombocytopenia; evans syndrome; jehovah's witness; thrombocytopenia; microangiopathic autoimmune hemolytic anemia; transfusion refusal; blood dyscrasia;

D O I：

10.7759/cureus.15508

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Evans syndrome (ES) is a rare hematologic disorder characterized by the development of autoimmune hemolytic anemia (AIHA), idiopathic thrombocytopenia, and occasionally immune-mediated neutropenia. Jehovah's Witnesses (JW) often decline blood product transfusion on the grounds of a scriptural stand based on biblical texts. The acute management of ES often consists of blood product transfusion in addition to high-dose steroids and intravenous immunoglobulin. We describe the case of a JW female presenting with new-onset, acutely worsening AIHA and thrombocytopenia with concern for hemodynamic compromise who was successfully treated with erythropoietin-stimulating agents, parenteral iron, folic acid, and high-dose steroids.

引用

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