The genetics of cystic fibrosis lung disease

被引:20
作者
Davidson, DJ [1 ]
Porteous, DJ [1 ]
机构
[1] Western Gen Hosp, MRC, Human Genet Unit, Edinburgh EH4 2XU, Midlothian, Scotland
关键词
D O I
10.1136/thx.53.5.389
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:389 / 397
页数:9
相关论文
共 54 条
[41]  
QUINTON PM, 1996, 2 J LEVY MEMORIAL LE, P1
[42]   MUCOCILIARY CLEARANCE IN PATIENTS WITH CYSTIC-FIBROSIS AND IN NORMAL SUBJECTS [J].
REGNIS, JA ;
ROBINSON, M ;
BAILEY, DL ;
COOK, P ;
HOOPER, P ;
CHAN, HK ;
GONDA, I ;
BAUTOVICH, G ;
BYE, PTP .
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 1994, 150 (01) :66-71
[43]   Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor [J].
Rozmahel, R ;
Wilschanski, M ;
Matin, A ;
Plyte, S ;
Oliver, M ;
Auerbach, W ;
Moore, A ;
Forstner, J ;
Durie, P ;
Nadeau, J ;
Bear, C ;
Tsui, LC .
NATURE GENETICS, 1996, 12 (03) :280-287
[44]  
SALMAN L, 1993, J CLIN INVEST, V92, P1875
[45]  
SANDERS A, 1997, LUNG SCI FDN, P2367
[46]  
SINGH P, 1997, PED PULM S, V14, P323
[47]   Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid [J].
Smith, JJ ;
Travis, SM ;
Greenberg, EP ;
Welsh, MJ .
CELL, 1996, 85 (02) :229-236
[48]   CFTR AS A CAMP-DEPENDENT REGULATOR OF SODIUM-CHANNELS [J].
STUTTS, MJ ;
CANESSA, CM ;
OLSEN, JC ;
HAMRICK, M ;
COHN, JA ;
ROSSIER, BC ;
BOUCHER, RC .
SCIENCE, 1995, 269 (5225) :847-850
[49]  
TSUI LC, 1992, CYSTIC FIBROSIS CURR, P27
[50]   Excessive inflammatory response of cystic fibrosis mice to bronchopulmonary infection with Pseudomonas aeruginosa [J].
van Heeckeren, A ;
Walenga, R ;
Konstan, MW ;
Bonfield, T ;
Davis, PB ;
Ferkol, T .
JOURNAL OF CLINICAL INVESTIGATION, 1997, 100 (11) :2810-2815