Caesarean Section under Gitelman Syndrome

被引：0

作者：

Rombach, Stephan ^{[1
]}

Benner, Alexander ^{[1
]}

Schick, Martin Alexander ^{[2
,3
]}

机构：

[1] Univ Klinikums Freiburg, Klin Anasthesiol & Intensivmed, Freiburg, Germany

[2] Univ Freiburg, Dept Anesthesiol & Crit Care, Med Ctr, Hugstetter Str 55, D-79106 Freiburg, Germany

[3] Univ Freiburg, Fac Med, Hugstetter Str 55, D-79106 Freiburg, Germany

来源：

ANASTHESIOLOGIE INTENSIVMEDIZIN NOTFALLMEDIZIN SCHMERZTHERAPIE | 2021年 / 56卷 / 04期

关键词：

anesthesiological management; Gitelman syndrome; metabolic disorder; nephrology; obstetrics; pregnancy; salt loss syndrome;

D O I：

10.1055/a-1299-0579

中图分类号：

R614 [麻醉学];

学科分类号：

100217 ;

摘要：

Gitelman syndrome is a rare inherited renal tubulopathy characterized by hypokalemia, hypomagnesemia and metabolic alcalosis. It is caused by a mutation in the SLC12A3 gene leading to a dysfunction of the thiazide-sensitive sodium chloride cotransporter and the magnesium transporters in the distal convoluted tubules. Only few reports of pregnant woman with Gitelman syndrome exist. Due to many unsolved questions about the impact on pregnancy and the maternal and fetal outcome, the obstetric and anesthesiological management remains a challenge. We discuss the case of a primary cesarean delivery in a 22-year-old woman with a new diagnosed Gitelman syndrome focusing on the anesthesiological approach. © 2021 Georg Thieme Verlag. All rights reserved.

引用

页码：289 / 295

页数：7

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