Endocrinopathies in the family of endoplasmic reticulum (ER) storage diseases: Disorders of protein trafficking and the role of ER molecular chaperones

被引:196
作者
Kim, PS
Arvan, P
机构
[1] Yeshiva Univ Albert Einstein Coll Med, Div Endocrinol, Bronx, NY 10461 USA
[2] Univ Cincinnati, Coll Med, Div Endocrinol, Cincinnati, OH 45267 USA
[3] Yeshiva Univ Albert Einstein Coll Med, Dept Dev & Mol Biol, Bronx, NY 10461 USA
关键词
D O I
10.1210/er.19.2.173
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:173 / 202
页数:30
相关论文
共 466 条
[41]   PERTURBATION OF CELLULAR CALCIUM INDUCES SECRETION OF LUMINAL ER PROTEINS [J].
BOOTH, C ;
KOCH, GLE .
CELL, 1989, 59 (04) :729-737
[42]   Chaperone function of Hsp90-associated proteins [J].
Bose, S ;
Weikl, T ;
Bugl, H ;
Buchner, J .
SCIENCE, 1996, 274 (5293) :1715-1717
[43]   ROLE OF ATP AND DISULFIDE BONDS DURING PROTEIN FOLDING IN THE ENDOPLASMIC-RETICULUM [J].
BRAAKMAN, I ;
HELENIUS, J ;
HELENIUS, A .
NATURE, 1992, 356 (6366) :260-262
[44]   MANIPULATING DISULFIDE BOND FORMATION AND PROTEIN FOLDING IN THE ENDOPLASMIC-RETICULUM [J].
BRAAKMAN, I ;
HELENIUS, J ;
HELENIUS, A .
EMBO JOURNAL, 1992, 11 (05) :1717-1722
[45]   THE NEUROENDOCRINE CHAPERONE 7B2 CAN ENHANCE IN-VITRO POMC CLEAVAGE BY PROHORMONE CONVERTASE PC2 [J].
BRAKS, JAM ;
MARTENS, GJM .
FEBS LETTERS, 1995, 371 (02) :154-158
[46]   Dissociation of the complex between the neuroendocrine chaperone 7B2 and prohormone convertase PC2 is not associated with proPC2 maturation [J].
Braks, JAM ;
vanHorssen, AM ;
Martens, GJM .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1996, 238 (02) :505-510
[47]   7B2 IS A NEUROENDOCRINE CHAPERONE THAT TRANSIENTLY INTERACTS WITH PROHORMONE CONVERTASE PC2 IN THE SECRETORY PATHWAY [J].
BRAKS, JAM ;
MARTENS, GJM .
CELL, 1994, 78 (02) :263-273
[48]  
BROWN G, 1992, SIGHT SOUND, V2, P43
[49]   The SREBP pathway: Regulation of cholesterol metabolism by proteolysis of a membrane-bound transcription factor [J].
Brown, MS ;
Goldstein, JL .
CELL, 1997, 89 (03) :331-340
[50]   RECYCLING RECEPTORS - THE ROUND-TRIP ITINERARY OF MIGRANT MEMBRANE-PROTEINS [J].
BROWN, MS ;
ANDERSON, RGW ;
GOLDSTEIN, JL .
CELL, 1983, 32 (03) :663-667