Dermatofibrosarcoma protuberans with fibrosarcomatous transformation: our experience, molecular evaluation of selected cases, and short literature review

被引：11

作者：

Lopez, Liurka V. ^{[1
]}

Yatsenko, Svetlana A. ^{[2
]}

Burgess, Melissa ^{[3
]}

Schoedel, Karen ^{[1
]}

Rao, Uma N. M. ^{[1
]}

机构：

[1] Univ Pittsburgh, Med Ctr, Shadyside Hosp, Bone & Soft Tissue Pathol Dept, 5230 Ctr Ave, Pittsburgh, PA 15232 USA

[2] Univ Pittsburgh, Magee Womens Hosp, Dept Obstet Gynecol & Reprod Sci, Pathol & Human Genet Pittsburgh Cytogenet Lab,Med, Pittsburgh, PA 15213 USA

[3] Univ Pittsburgh, Med Ctr, Hillman Canc Ctr, Div Hematol & Oncol, Pittsburgh, PA USA

来源：

INTERNATIONAL JOURNAL OF DERMATOLOGY | 2019年 / 58卷 / 11期

关键词：

LONG-TERM OUTCOMES; RADIATION; IMATINIB; MANAGEMENT; EFFICACY; EMPHASIS; SURGERY;

D O I：

10.1111/ijd.14462

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Dermatofibrosarcoma protuberans with fibrosarcomatous transformation (DFSP-FS) is a higher grade tumor arising from dermatofibrosarcoma protuberans (DFSP). Recent literature highlights its impact on recurrence rates, metastatic rates, and survival. In this article, we aim to describe our experience with 13 cases of DFSP-FS in terms of pathologic findings, molecular alterations, clinical outcomes, management, and also perform a short recent literature review.

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收藏

页码：1246 / 1252

页数：7

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