Chronic Pruritus in an 18-Month-Old Male Infant Due to Anicteric Cholestasis

被引：1

作者：

Nair, Vishnu S. ^{[1
]}

Chandrasekaran, Venkatesh ^{[1
]}

Jagadisan, Barath ^{[1
]}

Biswal, Niranjan ^{[1
]}

机构：

[1] JIPMER, Dept Paediat, Pondicherry 605006, India

来源：

JOURNAL OF TROPICAL PEDIATRICS | 2017年 / 63卷 / 04期

关键词：

chronic pruritus; anicteric cholestasis; infant; liver disease;

D O I：

10.1093/tropej/fmw084

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

An 18-month-old male infant was referred to us with pruritus from 6 months of age. He was being managed as atopic eczema with emollients and antihistamines without any response to treatment. On examination, he was found to have extensive scratch marks, mild hepatomegaly and no icterus. Blood investigations were suggestive of anicteric cholestatic liver disease. Liver biopsy was suggestive of progressive familial intrahepatic cholestasis type 3. He showed symptomatic improvement after starting ursodeoxycholic acid and fat-soluble vitamins and is under follow up.

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页码：321 / 323

页数：3

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