Biventricular pacing in an infant with noncompaction of the ventricular myocardium, congenital AV block, and prolonged QT interval

被引：6

作者：

Drago, Fabrizio ^{[1
]}

Silvetti, Massimo Stefano ^{[1
]}

Annichiarico, Marco ^{[1
]}

Michielon, Guido ^{[1
]}

Brancaccio, Gianluca ^{[1
]}

Zanoni, Stefano ^{[2
]}

Valsecchi, Sergio ^{[2
]}

机构：

[1] Bambino Gesu Pediat Hosp, Dept Pediat Cardiol, I-00165 Rome, Italy

[2] Medtron Italia, Rome, Italy

来源：

JOURNAL OF INTERVENTIONAL CARDIAC ELECTROPHYSIOLOGY | 2010年 / 28卷 / 01期

关键词：

Noncompacted ventricular myocardium; Congenital atrioventricular block; Dilated cardiomyopathy; CRT; Pediatrics; CARDIAC RESYNCHRONIZATION THERAPY; COMPLETE ATRIOVENTRICULAR-BLOCK; COMPLETE HEART-BLOCK; DILATED CARDIOMYOPATHY; CLINICAL-FEATURES; CHILDREN; PROGNOSIS; PATIENT;

D O I：

10.1007/s10840-009-9413-8

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

We describe the case of a newborn with isolated noncompaction of the ventricular myocardium, congenital atrioventricular block, and prolonged QT, who developed a dilated cardiomyopathy after 4 months of right ventricular permanent pacing. The implanted system was upgraded to biventricular pacing. Resynchronization therapy was associated with normalized septal motion and shortening of the interventricular delay and, within 2 months after initiation, resulted in markedly improved left ventricular ejection fraction and reduced ventricular volume.

引用

页码：67 / 70

页数：4

共 18 条

[1] Prediction of response to cardiac resynchronization therapy: The selection of candidates for CRT (SCART) study [J].

Achilli, Augusto ;

Peraldo, Carlo ;

Sassara, Massimo ;

Orazi, Serafino ;

Bianchi, Stefano ;

Laurenzi, Francesco ;

Donati, Roberto ;

Perego, Giovanni B. ;

Spampinato, Andrea ;

Valsecchi, Sergio ;

Denaro, Alessandra ;

Puglisi, Andrea .

PACE-PACING AND CLINICAL ELECTROPHYSIOLOGY, 2006, 29 :S11-S19

[2]

Buonanno C, 2000, Ital Heart J, V1, P301

[3] ISOLATED NONCOMPACTION OF LEFT-VENTRICULAR MYOCARDIUM - A STUDY OF 8 CASES [J].

CHIN, TK ;

PERLOFF, JK ;

WILLIAMS, RG ;

JUE, K ;

MOHRMANN, R .

CIRCULATION, 1990, 82 (02) :507-513

[4] Resynchronization therapy in pediatric and congenital heart disease patients - An international multicenter study [J].

Dubin, AM ;

Janousek, J ;

Rhee, E ;

Strieper, MJ ;

Cecchin, F ;

Law, IH ;

Shannon, KM ;

Temple, J ;

Rosenthal, E ;

Zimmerman, FJ ;

Davis, A ;

Karpawich, PP ;

Al Ahmad, A ;

Vetter, VL ;

Kertesz, NJ ;

Shah, M ;

Snyder, C ;

Stephenson, E ;

Emmel, M ;

Sanatani, S ;

Kanter, R ;

Batra, A ;

Collins, KK .

JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2005, 46 (12) :2277-2283

[5] Clinical features of isolated noncompaction of the ventricular myocardium - Long-term clinical course, hemodynamic properties, and genetic background [J].

Ichida, F ;

Hamamichi, Y ;

Miyawaki, T ;

Ono, Y ;

Kamiya, T ;

Akagi, T ;

Hamada, H ;

Hirose, O ;

Isobe, T ;

Yamada, K ;

Kurotobi, S ;

Mito, H ;

Miyake, T ;

Murakami, Y ;

Nishi, T ;

Shinohara, M ;

Seguchi, M ;

Tashiro, S ;

Tomimatsu, H .

JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1999, 34 (01) :233-240

[6] Myocardial ischaemia in children with isolated ventricular non-compaction [J].

Junga, G ;

Kneifel, S ;

Von Smekal, A ;

Steinert, H ;

Bauersfeld, U .

EUROPEAN HEART JOURNAL, 1999, 20 (12) :910-916

[7] Altered cardiac histology following apical right ventricular pacing in patients with congenital atrioventricular block [J].

Karpawich, PP ;

Rabah, R ;

Haas, JE .

PACE-PACING AND CLINICAL ELECTROPHYSIOLOGY, 1999, 22 (09) :1372-1377

[8] Cardiac resynchronization therapy in a patient with isolated noncompaction of the left ventricle and a narrow QRS complex [J].

Kubota, Shoichi ;

Nogami, Akihiko ;

Sugiyasu, Aiko ;

Kasuya, Kenji .

HEART RHYTHM, 2006, 3 (05) :619-620

[9] Clinical features of isolated noncompaction of the myocardium in children [J].

Neudorf, UE ;

Hussein, A ;

Trowitzsch, E ;

Schmaltz, AA .

CARDIOLOGY IN THE YOUNG, 2001, 11 (04) :439-442

[10] Long-term follow-up of 34 adults with isolated left ventricular noncompaction: A distinct cardiomyopathy with poor prognosis [J].

Oechslin, EN ;

Jost, CHA ;

Rojas, JR ;

Kaufmann, PA ;

Jenni, R .

JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 2000, 36 (02) :493-+

← 1 2 →