Prevasculitic Eosinophilic Granulomatosis With Polyangiitis

被引:1
|
作者
Burtson, Kathryn M. [1 ]
Bishop, Jonathan [2 ]
机构
[1] Wright State Univ, Internal Med, Dayton, OH 45435 USA
[2] Univ Pittsburgh, Med Ctr Mercy, Crit Care Med, Pittsburgh, PA USA
关键词
churg-strauss syndrome; vasculitis; prevasculitic stage; eosinophilia; eosinophilic gastritis; eosinophilic duodenitis;
D O I
10.7759/cureus.14649
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Eosinophilic granulomatosis with polyangiitis (EGPA) is an exceptionally rare systemic necrotizing vasculitis. The disease is clinically characterized by asthma with concomitant blood and tissue eosinophilia, often progressing to eosinophilic vasculitis. From the Onset of asthma, there is usually a three to nine year delay of EGPA diagnosis. We report a case of this highly uncommon disease identified in an early stage.
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页数:5
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