Adolescent case of Alexander disease: MR imaging and MR spectroscopy

被引:19
作者
Takanashi, J
Sugita, K
Tanabe, Y
Niimi, H
机构
[1] Chiba Univ, Fac Med, Dept Pediat, Chuo Ku, Chiba 260, Japan
[2] Chiba Childrens Hosp, Div Neurol, Chiba, Japan
关键词
D O I
10.1016/S0887-8994(97)00128-8
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 17-year-old male was diagnosed as having Alexander disease from the clinical manifestations (psychomotor deterioration and megalencephaly), neuroradiologic findings (frontal dominant leukodystrophy), and elevation of alpha B-crystallin and heat shock protein 27 in the cerebrospinal fluid, He exhibited increased attenuation on computed tomography and T-1 and T-2 shortening on magnetic resonance imaging in the bilateral basal ganglia and thalamus. Some paramagnetic substances might be deposited in the basal ganglia and thalamus in the late stage of Alexander disease, at least 8 years after onset. (C) 1998 by Elsevier Science Inc. All rights reserved.
引用
收藏
页码:67 / 70
页数:4
相关论文
共 14 条
[1]   NORMAL DEPOSITION OF BRAIN IRON IN CHILDHOOD AND ADOLESCENCE - MR IMAGING AT 1.5 T [J].
AOKI, S ;
OKADA, Y ;
NISHIMURA, K ;
BARKOVICH, AJ ;
KJOS, BO ;
BRASCH, RC ;
NORMAN, D .
RADIOLOGY, 1989, 172 (02) :381-385
[2]   LOCALIZED H-1-NMR SPECTROSCOPY IN CANAVANS DISEASE - A REPORT OF 2 CASES [J].
AUSTIN, SJ ;
CONNELLY, A ;
GADIAN, DG ;
BENTON, JS ;
BRETT, EM .
MAGNETIC RESONANCE IN MEDICINE, 1991, 19 (02) :439-445
[3]   MRI AND CT IN KRABBES DISEASE - CASE-REPORT [J].
BERNARDI, B ;
FONDA, C ;
FRANZONI, E ;
MARCHIANI, V ;
DELLAGUISTINA, E ;
ZIMMERMAN, RA .
NEURORADIOLOGY, 1994, 36 (06) :477-479
[4]   COMPUTED-TOMOGRAPHY IN ALEXANDERS DISEASE [J].
FARRELL, K ;
CHUANG, S ;
BECKER, LE .
ANNALS OF NEUROLOGY, 1984, 15 (06) :605-607
[5]   CHANGES IN THE BASAL GANGLIA AND THALAMUS FOLLOWING REPERFUSION AFTER COMPLETE CEREBRAL-ISCHEMIA [J].
FUJIOKA, M ;
OKUCHI, K ;
MIYAMOTO, S ;
SAKAKI, T ;
HIRAMATSU, K ;
TOMINAGA, M ;
KAMADA, Y ;
IWASAKI, S .
NEURORADIOLOGY, 1994, 36 (08) :605-607
[6]   METABOLIC AND DESTRUCTIVE BRAIN DISORDERS IN CHILDREN - FINDINGS WITH LOCALIZED PROTON MR SPECTROSCOPY [J].
GRODD, W ;
KRAGELOHMANN, I ;
KLOSE, U ;
SAUTER, R .
RADIOLOGY, 1991, 181 (01) :173-181
[7]   USE OF COMPUTED-TOMOGRAPHY, MAGNETIC-RESONANCE-IMAGING, AND LOCALIZED 1H MAGNETIC-RESONANCE SPECTROSCOPY IN CANAVANS DISEASE - A CASE-REPORT [J].
MARKS, HG ;
CARO, PA ;
WANG, ZY ;
DETRE, JA ;
BOGDAN, AR ;
GUSNARD, DA ;
ZIMMERMAN, RA .
ANNALS OF NEUROLOGY, 1991, 30 (01) :106-110
[8]  
NISHIMURA A, 1994, NO TO HATTATSU, V26, pS155
[9]   INCREMENT OF ALPHA B-CRYSTALLIN MESSENGER-RNA IN THE BRAIN OF PATIENT WITH INFANTILE TYPE ALEXANDERS DISEASE [J].
OCHI, N ;
KOBAYASHI, K ;
MAEHARA, M ;
NAKAYAMA, A ;
NEGORO, T ;
SHINOHARA, H ;
WATANABE, K ;
NAGATSU, T ;
KATO, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1991, 179 (02) :1030-1035
[10]   ALEXANDERS DISEASE - REPORT AND REAPPRAISAL [J].
RUSSO, LS ;
ARON, A ;
ANDERSON, PJ .
NEUROLOGY, 1976, 26 (07) :607-614