[1] F CRIN INNOVTE, F-42055 St Etienne 2, France
[2] Univ Montpellier, CHU Montpellier, Hop St Eloi, EA2992,Dept Med Vasc,Ctr Reference Malad Vasc Rar, F-34295 Montpellier, France
[3] Univ Toronto, Sunnybrook Hlth Sci Ctr, Dept Med, Toronto, ON, Canada
[4] Hop Europeen Georges Pompidou, Serv Pneumol & Soins Intensifs, 20 Rue Leblanc, F-75015 Paris, France
[5] INSERM, Innovat Therapeut Hemostase, UMRS 1140, F-75006 Paris, France