Clinical implications and possible association of malposition of the branch pulmonary arteries with DiGeorge syndrome and microdeletion of chromosomal region 22q11

被引：28
作者：
Recto, MR [1 ]
Parness, IA [1 ]
Gelb, BD [1 ]
Lopez, L [1 ]
Lai, WW [1 ]
机构：
[1] MT SINAI MED CTR,DIV PEDIAT CARDIOL,NEW YORK,NY 10029
来源：
AMERICAN JOURNAL OF CARDIOLOGY | 1997年 / 80卷 / 12期
关键词：
D O I：
10.1016/S0002-9149(97)00782-0
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We describe a series of 10 patients with malposition of the branch pulmonary arteries (4 patients with crossing [crossed pulmonary arteries] and 6 patients without crossing), 2 of whom had a short main pulmonary artery segment that resulted in iatrogenic right pulmonary artery stenosis after pulmonary artery band placement. DiGeorge syndrome was seen in 5 patients and 4 had microscopic deletion of chromosomal region 22q11.
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页码：1624 / &
页数：6
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