Lymphomatoid granulomatosis in a 4-year-old boy

被引:7
作者
LeSueur, BW [1 ]
Ellsworth, L [1 ]
Bangert, JL [1 ]
Hansen, RC [1 ]
机构
[1] Univ Arizona, Coll Med, Dermatol Sect, Tucson, AZ USA
关键词
D O I
10.1046/j.1525-1470.2000.017005369.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Lymphomatoid granulomatosis is a necrotizing angiocentric and angiodestructive infiltrative process involving primarily the lung, skin, central nervous system, and kidney. The incidence is highest in middle-aged men and is rare in children. We report a case of lymphomatoid granulomatosis involving both skin and lung in a 4-year-old boy. The disease progressed to peripheral T-cell lymphoma, which was unusual in light of recent evidence suggesting a a-cell origin in the majority of cases.
引用
收藏
页码:369 / 372
页数:4
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