Thrombotic thrombocytopenic purpura in a new onset lupus patient?

被引：3

作者：

Sablon Gonzalez, Nery ^{[1
]}

Lorenzo, Noel ^{[2
]}

Parodis, Yanet ^{[1
]}

Alonso Ortiz, Maria Belen ^{[1
]}

Kechida, Melek ^{[3
]}

Rodriguez Perez, Jose Carlos ^{[1
]}

机构：

[1] Hosp Univ Gran Canaria Dr Negrin, Las Palmas Gran Canaria, Spain

[2] Ctr Hosp St Cyr, Lyon, France

[3] Hop Univ Fattouma Bourguiba, Monastir, Tunisia

来源：

IMMUNOLOGIC RESEARCH | 2017年 / 65卷 / 02期

关键词：

Thrombotic thrombocytopenic purpura; Microangiopathic hemolytic anemia; Lupus; ERYTHEMATOSUS; MANAGEMENT; NEPHRITIS; REGISTRY;

D O I：

10.1007/s12026-017-8898-y

中图分类号：

R392 [医学免疫学]; Q939.91 [免疫学];

学科分类号：

100102 ;

摘要：

We are presenting a case of TTP with undetectable levels of ADAMTS 13 in a 39-year-old woman. Diagnosis of systemic lupus was evoked in the setting of thrombotic microangiopathy. The patient presented normal renal function but important neurological impairment. Treatment with daily plasmapheresis as well as Rituximab, cyclophosphamide as steroids was required to achieve clinical improvement.

引用

页码：454 / 458

页数：5

共 18 条

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