A case of solitary median maxillary central incisor (SMMCI) syndrome with bilateral pyriform aperture stenosis and choanal atresia

被引：16
作者：
Blackmore, Kate [1 ]
Wynne, David M. [1 ]
机构：
[1] Royal Hosp Sick Children, Dept ENT, Glasgow G3 8SJ, Lanark, Scotland
来源：
INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY | 2010年 / 74卷 / 08期
关键词：
Solitary median maxillary central incisor syndrome; Congenital pyriform aperture stenosis; Choanal atresia; Nasal obstruction;
D O I：
10.1016/j.ijporl.2010.05.018
中图分类号：
R76 [耳鼻咽喉科学];
学科分类号：
100213 ;
摘要：
Solitary median maxillary central incisor syndrome is a rare disorder involving midline abnormalities. It may present with life threatening respiratory distress in the neonate secondary to nasal malformations. These include pyriform aperture stenosis and choanal atresia. We present the first reported case of simultaneous choanal atresia and pyriform aperture stenosis in a neonate with solitary median maxillary central incisor syndrome. The clinical presentation and the management of congenital pyriform aperture stenosis are discussed. (C) 2010 Elsevier Ireland Ltd. All rights reserved.
引用
收藏
页码：967 / 969
页数：3
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