Treatment of the Crigler-Najjar syndrome type I with hepatocyte transplantation

被引:764
作者
Fox, IJ
Chowdhury, JR
Kaufman, SS
Goertzen, TC
Chowdhury, NR
Warkentin, PI
Dorko, K
Sauter, BV
Strom, SC
机构
[1] Univ Nebraska, Med Ctr, Dept Surg, Omaha, NE 68198 USA
[2] Univ Nebraska, Med Ctr, Dept Pediat, Omaha, NE 68198 USA
[3] Univ Nebraska, Med Ctr, Dept Radiol, Omaha, NE 68198 USA
[4] Univ Nebraska, Med Ctr, Dept Pathol & Lab Med, Omaha, NE 68198 USA
[5] Albert Einstein Coll Med, Dept Med, New York, NY USA
[6] Albert Einstein Coll Med, Dept Mol Genet, New York, NY USA
[7] Albert Einstein Coll Med, Marion Bessin Liver Res Ctr, New York, NY USA
[8] Univ Pittsburgh, Sch Med, Dept Pathol, Pittsburgh, PA USA
关键词
D O I
10.1056/NEJM199805143382004
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:1422 / 1426
页数:5
相关论文
共 23 条
[1]   PRINCIPLES OF SOLID-ORGAN PRESERVATION BY COLD-STORAGE [J].
BELZER, FO ;
SOUTHARD, JH .
TRANSPLANTATION, 1988, 45 (04) :673-676
[2]   Intrasplenic hepatocyte allotransplantation in dalmatian dogs with and without cyclosporine immunosuppression [J].
Benedetti, E ;
Kirby, JP ;
Asolati, M ;
Blanchard, J ;
Ward, MG ;
Williams, R ;
Hewett, TA ;
Fontaine, M ;
Pollak, R .
TRANSPLANTATION, 1997, 63 (09) :1206-1209
[3]  
Bilir B., 1996, Hepatology, V24, p308A
[4]   Population expansion, clonal growth, and specific differentiation patterns in primary cultures of hepatocytes induced by HGF/SF, EGF and TGF alpha in a chemically defined (HGM) medium [J].
Block, GD ;
Locker, J ;
Bowen, WC ;
Petersen, BE ;
Katyal, S ;
Strom, SC ;
Riley, T ;
Howard, TA ;
Michalopoulos, GK .
JOURNAL OF CELL BIOLOGY, 1996, 132 (06) :1133-1149
[5]   THE GENETIC-BASIS OF THE REDUCED EXPRESSION OF BILIRUBIN UDP-GLUCURONOSYLTRANSFERASE-1 IN GILBERTS-SYNDROME [J].
BOSMA, PJ ;
CHOWDHURY, JR ;
BAKKER, C ;
GANTLA, S ;
DEBOER, A ;
OOSTRA, BA ;
LINDHOUT, D ;
TYTGAT, GNJ ;
JANSEN, PLM ;
ELFERINK, RPJO ;
CHOWDHURY, NR .
NEW ENGLAND JOURNAL OF MEDICINE, 1995, 333 (18) :1171-1175
[6]  
CHOWDHURY J R, 1981, Hepatology, V1, P622
[7]  
CRIGLER JF, 1952, PEDIATRICS, V10, P169
[8]   UNCONJUGATED BILIRUBIN AND AN INCREASED PROPORTION OF BILIRUBIN MONO-CONJUGATES IN BILE OF PATIENTS WITH GILBERTS SYNDROME AND CRIGLER-NAJJAR DISEASE [J].
FEVERY, J ;
BLANCKAERT, N ;
HEIRWEGH, KPM ;
PREAUX, AM ;
BERTHELOT, P .
JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (05) :970-979
[9]   CONDITIONAL IMMORTALIZATION OF GUNN RAT HEPATOCYTES - AN EX-VIVO MODEL FOR EVALUATING METHODS FOR BILIRUBIN-UDP-GLUCURONOSYLTRANSFERASE GENE-TRANSFER [J].
FOX, IJ ;
CHOWDHURY, NR ;
GUPTA, S ;
KONDAPALLI, R ;
SCHILSKY, ML ;
STOCKERT, RJ ;
CHOWDHURY, JR .
HEPATOLOGY, 1995, 21 (03) :837-846
[10]  
FOX IJ, 1997, ACUTE LIVER FAILURE, P285