A 19-year-old man visited our hospital because of diarrhea and blood and liver dysfunction. Magnetic and endoscopic retrograde cholangiography revealed diffuse narrowing of the common biliary tract and intrahepatic biliary tract. A biopsy specimen from the narrowed area of the common biliary tract revealed IgG4-related sclerosing cholangitis (IgG4-SC). Colonoscopy showed multiple aphthoid colitis. He was treated with corticosteroids, and the levels of hepatobiliary enzymes, IgG, and IgG4 gradually decreased. This is an extremely rare case of colitis in which the patient had a phenotype of sclerosing cholangitis similar to IgG4-SC, which was finally diagnosed as primary sclerosing cholangitis.
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Sungkyunkwan Univ, Dept Med, Samsung Med Ctr, Sch Med, 81 Irwon Ro, Seoul, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Woo, Young Sik
Cho, Dong Hui
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Cho, Dong Hui
Oh, Dongwook
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Oh, Dongwook
Song, Tae Jun
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Song, Tae Jun
Park, Do Hyun
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Park, Do Hyun
Lee, Sang Soo
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Lee, Sang Soo
Seo, Dong Wan
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
Seo, Dong Wan
Lee, Sung Koo
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Univ Ulsan, Dept Internal Med, Asan Med Ctr, Coll Med, Asanbyeongwon Gil 86, Seoul 138736, South KoreaHallym Univ, Sacred Heart Hosp, Dept Internal Med, Coll Med, Anyang, South Korea
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Tokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, JapanTokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, Japan
Kamisawa, Terumi
Tabata, Taku
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Tokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, JapanTokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, Japan
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Swedish Med Ctr, Liver Care Network & Organ Care Res, Seattle, WA 98122 USASwedish Med Ctr, Liver Care Network & Organ Care Res, Seattle, WA 98122 USA
Shah, Raj A.
Kowdley, Kris V.
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Swedish Med Ctr, Liver Care Network & Organ Care Res, Seattle, WA 98122 USASwedish Med Ctr, Liver Care Network & Organ Care Res, Seattle, WA 98122 USA
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Japanese Red Cross Nagoya Daini Hosp, Dept Gastroenterol, 2-9 Myoken Cho Showa Ku, Nagoya, Aichi 4668650, JapanJapanese Red Cross Nagoya Daini Hosp, Dept Gastroenterol, 2-9 Myoken Cho Showa Ku, Nagoya, Aichi 4668650, Japan
Nakazawa, Takahiro
Shimizu, Shuya
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Japanese Red Cross Nagoya Daini Hosp, Dept Gastroenterol, 2-9 Myoken Cho Showa Ku, Nagoya, Aichi 4668650, JapanJapanese Red Cross Nagoya Daini Hosp, Dept Gastroenterol, 2-9 Myoken Cho Showa Ku, Nagoya, Aichi 4668650, Japan
Shimizu, Shuya
Naitoh, Itaru
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi, JapanJapanese Red Cross Nagoya Daini Hosp, Dept Gastroenterol, 2-9 Myoken Cho Showa Ku, Nagoya, Aichi 4668650, Japan
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Nagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, JapanNagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, Japan
Naitoh, Itaru
Hayashi, Kazuki
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Nagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, JapanNagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, Japan
Hayashi, Kazuki
Miyabe, Katsuyuki
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Nagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, JapanNagoya City Univ, Dept Gastroenterol & Metab, Grad Sch Med Sci, Nagoya, Aichi 4678601, Japan
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Naitoh, Itaru
Nakazawa, Takahiro
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Nakazawa, Takahiro
Hayashi, Kazuki
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Hayashi, Kazuki
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Miyabe, Katsuyuki
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Shimizu, Shuya
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Kondo, Hiromu
Nishi, Yuji
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Nishi, Yuji
Yoshida, Michihiro
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Yoshida, Michihiro
Umemura, Shuichiro
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Umemura, Shuichiro
Hori, Yasuki
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Hori, Yasuki
Kato, Akihisa
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Kato, Akihisa
Okumura, Fumihiro
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Gifu Prefectural Tajimi Hosp, Dept Gastroenterol, Tajimi, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Okumura, Fumihiro
Sano, Hitoshi
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Gifu Prefectural Tajimi Hosp, Dept Gastroenterol, Tajimi, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Sano, Hitoshi
Ohara, Hirotaka
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Nagoya City Univ, Grad Sch Med Sci, Dept Community Based Med Educ, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan
Ohara, Hirotaka
Joh, Takashi
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Nagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, JapanNagoya City Univ, Grad Sch Med Sci, Dept Gastroenterol & Metab, Nagoya, Aichi 4678601, Japan