A cutaneous thickening case ...

被引：0

作者：

Serra, S. ^{[1
]}

Ambrosio, C. ^{[1
]}

Salvador, M. Joao ^{[1
]}

Silva, J. ^{[1
]}

Serra, D. ^{[2
]}

Reis, J. Pedro ^{[2
]}

Malcata, A. ^{[1
]}

机构：

[1] Hosp Univ Coimbra, Serv Reumatol, P-3000 Coimbra, Portugal

[2] Hosp Univ Coimbra, Serv Dermatol, P-3000 Coimbra, Portugal

来源：

ACTA REUMATOLOGICA PORTUGUESA | 2010年 / 35卷 / 01期

关键词：

Cutaneous thickening; Scleroderma-like Disorders; Scleromyxedema; Skin Biopsy; STEM-CELL TRANSPLANTATION; HIGH-DOSE DEXAMETHASONE; SCLEROMYXEDEMA; DISORDERS;

D O I：

暂无

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The authors present a clinical case of a 79 years old female patient, with a progressive cutaneous thickening of the face, trunk and limbs, lasting for 6 years. She also presented exertional dyspnea and intermittent solid dysphagia. The laboratory study identified IgG KAPA monoclonal protein and antinuclear antibodies with a speckled pattern. The nailfold capillaroscopy was normal. A detailed physical examination together with cutaneous histopathology led to the diagnosis of Scleromyxedema, a rare cutaneous scleroderma like disease. The differential diagnosis of cutaneous sclerosis is discussed.

引用

页码：66 / 71

页数：6

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