New type of epidermal nevus syndrome

被引:7
作者
Gobello, T
Mazzanti, C
Zambruno, G
Chinni, LM
Happle, R
机构
[1] IRCCS, Ist Dermopat Immacolata, Lab Mol & Cell Biol, I-00167 Rome, Italy
[2] IRCCS, Ist Dermopat Immacolata, Dermatol Div 8, I-00167 Rome, Italy
[3] Univ Marburg, Dept Dermatol, D-35032 Marburg, Germany
关键词
epidermal nevus syndrome; bone abnormalities; hyperkeratosis; onychodystrophy; hypertrichosis;
D O I
10.1159/000018431
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
An uncommon type of epidermal nevus characterized by systematized bands of non-epidermolytic hyperkeratosis with increased hairiness and follicular hyperkeratosis was observed in a 16-year-old boy who showed, in addition, hemihypoplasia of limbs, brachydactyly, clinodactyly and onychodystrophy. This case cannot be categorized within the group of presently established epidermal nevus syndromes. Most likely, this combination of anomalies represents a new type of epidermal nevus syndrome. Copyright (C) 2000 S. Karger AG, Basel.
引用
收藏
页码:51 / 53
页数:3
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