ATYPICAL CHILDHOOD CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY

被引:5
|
作者
Mohamed, Ahmad R. [1 ]
Rodriguez-Casero, M. Victoria [1 ]
Ryan, Monique M. [1 ,2 ,3 ]
机构
[1] Royal Childrens Hosp, Childrens Neurosci Ctr, Parkville, Vic 3052, Australia
[2] Royal Childrens Hosp, Murdoch Childrens Res Inst, Parkville, Vic 3052, Australia
[3] Univ Melbourne, Dept Paediat, Parkville, Vic 3052, Australia
关键词
atypical; child; CIDP; diagnostic criteria; empiric treatment; CLINICAL-COURSE; POLYRADICULONEUROPATHY; CRITERIA;
D O I
10.1002/mus.21703
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Chronic inflammatory demyelinating polyneuropathy (CIDP) is an uncommon cause of progressive weakness in childhood. The diagnosis is easy when the clinical history and findings are supported by unequivocal electrophysiologic and laboratory evidence of demyelination, but it can be challenging if the criteria for demyelination are not met. We report a case of atypical childhood CIDP to highlight the diagnostic difficulties and the importance of recognizing this treatable condition. Muscle Nerve 42: 293-295, 2010
引用
收藏
页码:293 / 295
页数:3
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