Esophageal variceal bleeding caused by hypoplasia of the portal vein in a patient with the Klippel-Trenaunay syndrome

被引:12
作者
Bataller, R [1 ]
Sans, M [1 ]
Escorsell, A [1 ]
Elizalde, JI [1 ]
Bosch, J [1 ]
Rodés, J [1 ]
机构
[1] Univ Barcelona, Hosp Clin & Prov, Liver Unit, Barcelona 08036, Spain
关键词
D O I
10.1111/j.1572-0241.1998.270_5.x
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
The case of a patient affected by Klippel-Trenaunay syndrome presenting with esophageal variceal bleeding caused by hypoplasia of the vena porta is reported, Hemostasis was achieved by performing a proximal spleno-renal shunt, We discuss the likely association of this mesodermal development abnormality and vascular disorders of the portal vein. (C) 1998 by Am. Coll. of Gastroenterology.
引用
收藏
页码:275 / 276
页数:2
相关论文
共 9 条
[1]   JEJUNAL VASCULAR MALFORMATION IN KLIPPEL-TRENAUNAY-SYNDROME [J].
BROWN, R ;
OHRI, SK ;
GHOSH, P ;
JACKSON, J ;
SPENCER, J ;
ALLISON, D .
CLINICAL RADIOLOGY, 1991, 44 (02) :134-136
[2]  
GLOVICZKI P, 1991, SURGERY, V110, P469
[3]   MULTIPLE FOCAL NODULAR HYPERPLASIA OF THE LIVER ASSOCIATED WITH HEMIHYPERTROPHY AND VASCULAR MALFORMATIONS [J].
HABER, M ;
REUBEN, A ;
BURRELL, M ;
OLIVERIO, P ;
SALEM, RR ;
WEST, AB .
GASTROENTEROLOGY, 1995, 108 (04) :1256-1262
[4]  
KAISE M, 1992, GASTROENTEROL JPN, V27, P546
[5]   TREATMENT OF COLONIC BLEEDING IN KLIPPEL-TRENAUNAY-SYNDROME WITH COMBINED PARTIAL COLECTOMY AND ENDOSCOPIC LASER [J].
MYERS, BM .
DIGESTIVE DISEASES AND SCIENCES, 1993, 38 (07) :1351-1353
[6]   THE KLIPPEL-TRENAUNAY-SYNDROME ASSOCIATED WITH RENAL-ARTERY ANEURYSM [J].
OGDEN, CW ;
JACKSON, JE .
BRITISH JOURNAL OF UROLOGY, 1993, 71 (05) :617-618
[7]  
SCHITT B, 1986, J PEDIAT GASTROENTER, V5, P155
[8]   KLIPPEL-TRENAUNAY AND STURGE-WEBER SYNDROMES WITH RENAL HEMANGIOMA AND DOUBLE INFERIOR VENA-CAVA [J].
SCHOFIELD, D ;
ZAATARI, GS ;
GAY, BB .
JOURNAL OF UROLOGY, 1986, 136 (02) :442-445
[9]   STURGE-WEBER AND KLIPPEL-TRENAUNY SYNDROMES WITH ABSENCE OF INFERIOR VENA-CAVA [J].
STEWART, G ;
FARMER, G .
ARCHIVES OF DISEASE IN CHILDHOOD, 1990, 65 (05) :546-547