Outcome in infant with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation

被引:47
作者
Powell, AJ
Mayer, JE
Lang, P
Lock, JE
机构
[1] Childrens Hosp, Dept Cardiol, Boston, MA 02115 USA
[2] Childrens Hosp, Dept Cardiac Surg, Boston, MA 02115 USA
[3] Harvard Univ, Sch Med, Dept Pediat, Boston, MA 02115 USA
[4] Harvard Univ, Sch Med, Dept Surg, Boston, MA 02115 USA
关键词
D O I
10.1016/S0002-9149(00)01220-0
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Management of all patients with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation (n = 12) with staged surgery directed toward a Fontan palliation resulted in an 83% 5-year actuarial survival. Both deaths in the study were presumably related to coronary ischemia and occurred in the first 4 months of life.
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页码:1272 / +
页数:4
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