Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog

被引：25

作者：

Rychik, Jack ^{[1
]}

Dodds, Kathryn M. ^{[1
]}

Goldberg, David ^{[1
]}

Glatz, Andrew C. ^{[1
]}

Fogel, Mark ^{[1
]}

Rossano, Joseph ^{[1
]}

Chen, Jonathan ^{[1
]}

Pinto, Erin ^{[1
]}

Ravishankar, Chitra ^{[1
]}

Rand, Elizabeth ^{[1
]}

Rome, Jonathan J. ^{[1
]}

Dori, Yoav ^{[1
]}

机构：

[1] Childrens Hosp Philadelphia, Cardiac Ctr, 3401 Civ Ctr Blvd, Philadelphia, PA 19104 USA

来源：

WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY | 2020年 / 11卷 / 01期

关键词：

Fontan; lymphatics; protein losing enteropathy; single ventricle; THORACIC-DUCT;

D O I：

10.1177/2150135119890555

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.

引用

页码：92 / 96

页数：5

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