Difficult Diagnosis of Atypical Cystic Pancreatic Lesions in von Hippel-Lindau Disease

被引:6
|
作者
Neuzillet, Cindy
Vullierme, Marie-Pierre [1 ]
Couvelard, Anne [2 ]
Sauvanet, Alain
Levy, Philippe
Richard, Stephane [3 ]
Ruszniewski, Philippe
Hammel, Pascal [1 ]
机构
[1] Hop Beaujon, Serv Radiol, F-92110 Clichy, France
[2] Hop Beaujon, Serv Anatomopathol, F-92110 Clichy, France
[3] Hop Bicetre, Serv Urol, Le Kremlin Bicetre, France
关键词
von Hippel-Lindau disease; pancreas; pancreatic cyst; endocrine tumor; radiology; imaging; surgical resection; NEUROENDOCRINE TUMORS; CLINICAL-SIGNIFICANCE; CHROMOGRANIN-A; INVOLVEMENT; MANAGEMENT; SPECTRUM; FEATURES; CT;
D O I
10.1097/RCT.0b013e3181b52b84
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
von Hippel-Lindau disease is a progressive, autosomal dominant disorder with multiorgan involvement. There are 2 types of pancreatic lesions from von Hippel-Lindau disease: cystic lesions and endocrine pancreatic tumors. Only the latter type is potentially malignant and may justify pancreatic resection. The differential diagnosis between these 2 types of lesions can be difficult. We report 3 patients with atypical cystic pancreatic lesions who underwent surgery for suspected malignant tumors. The pathological-radiological correlations and the diagnostic and management strategies are discussed.
引用
收藏
页码:140 / 145
页数:6
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