Papillary adenoma of endolymphatic sac origin: a temporal bone tumor in von Hippel-Lindau disease - Case report

被引:15
作者
Ouallet, JC
MarsotDupuch, K
VanEffenterre, R
Kujas, M
Tubiana, JM
机构
[1] HOP ST ANTOINE,SERV RADIOL,DEPT RADIOL,F-75012 PARIS,FRANCE
[2] HOP LA PITIE SALPETRIERE,DEPT NEUROSURG,PARIS,FRANCE
[3] HOP PITIE,DEPT HISTOL,F-75651 PARIS,FRANCE
关键词
endolymphatic sac; temporal bone tumor; magnetic resonance imaging; vonHippel Lindau disease; ear;
D O I
10.3171/jns.1997.87.3.0445
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
This report describes a patient with von Hippel-Lindau disease who presented with an g-year history of a slow-growing, locally invasive vascularized lesion of the temporal bone involving the cerebellopontine angle. The mass, studied by computerized tomography scanning and magnetic resonance imaging techniques, was partly cystic in appearance. After removal of the mass, pathological studies confirmed a papillary cystic tumor with characteristics that have been described in tumors with an endolymphatic sac origin. These rare neoplasms constitute a distinct pathological entity and deserve wider recognition.
引用
收藏
页码:445 / 449
页数:5
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