Mechanisms of disease - Pathogenesis and treatment of sickle cell disease

被引：739
作者：
Bunn, HF [1 ]
机构：
[1] HARVARD UNIV, BRIGHAM & WOMENS HOSP, SCH MED, DIV HEMATOL, BOSTON, MA 02115 USA
来源：
NEW ENGLAND JOURNAL OF MEDICINE | 1997年 / 337卷 / 11期
关键词：
D O I：
10.1056/NEJM199709113371107
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
[No abstract available]
引用
收藏
页码：762 / 769
页数：8
相关论文
共 73 条
[1]   PHYSIOLOGICAL AND X-RAY STUDIES OF POTENTIAL ANTISICKLING AGENTS [J].
ABRAHAM, DJ ;
PERUTZ, MF ;
PHILLIPS, SEV .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (02) :324-328
[2]  
al-Khatti A, 1988, Trans Assoc Am Physicians, V101, P54
[3]   PARTIALLY OXYGENATED SICKLED CELLS - SICKLE-SHAPED RED-CELLS FOUND IN CIRCULATING BLOOD OF PATIENTS WITH SICKLE-CELL DISEASE [J].
ASAKURA, T ;
MATTIELLO, JA ;
OBATA, K ;
ASAKURA, K ;
REILLY, MP ;
TOMASSINI, N ;
SCHWARTZ, E ;
OHENEFREMPONG, K .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (26) :12589-12593
[4]   EFFECT OF HYDROXYUREA ON THE RHEOLOGICAL PROPERTIES OF SICKLE ERYTHROCYTES INVIVO [J].
BALLAS, SK ;
DOVER, GJ ;
CHARACHE, S .
AMERICAN JOURNAL OF HEMATOLOGY, 1989, 32 (02) :104-111
[5]  
BARABINO GA, 1987, BLOOD, V70, P152
[6]   THE EFFECTS OF ALPHA-CHAIN MUTATIONS CIS AND TRANS TO THE BETA-6 MUTATION ON THE POLYMERIZATION OF SICKLE-CELL HEMOGLOBIN [J].
BENESCH, RE ;
KWONG, S ;
BENESCH, R .
NATURE, 1982, 299 (5880) :231-234
[7]   A multiparameter analysis of sickle erythrocytes in patients undergoing hydroxyurea therapy [J].
Bridges, KR ;
Barabino, GD ;
Brugnara, C ;
Cho, MR ;
Christoph, GW ;
Dover, G ;
Ewenstein, BM ;
Golan, DE ;
Guttmann, CRG ;
Hofrichter, J ;
Mulkern, RV ;
Zhang, B ;
Eaton, WA .
BLOOD, 1996, 88 (12) :4701-4710
[8]  
BRITTAIN HA, 1993, BLOOD, V81, P2137
[9]   REGULATION OF CATION CONTENT AND CELL-VOLUME IN HEMOGLOBIN ERYTHROCYTES FROM PATIENTS WITH HOMOZYGOUS HEMOGLOBIN-C DISEASE [J].
BRUGNARA, C ;
KOPIN, AS ;
BUNN, HF ;
TOSTESON, DC .
JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (05) :1608-1617
[10]   REGULATION OF ERYTHROCYTE CATION AND WATER-CONTENT IN SICKLE-CELL-ANEMIA [J].
BRUGNARA, C ;
BUNN, HF ;
TOSTESON, DC .
SCIENCE, 1986, 232 (4748) :388-390
12345678