Primary tumors of the heart are exceedingly rare with a prevalence rate of around 0.01% in autopsy studies. A majority of primary cardiac tumors are benign. Rhabdomyomas are the most common of benign pediatric cardiac tumors. A newborn female infant presented with perioral cyanosis and respiratory distress. She deteriorated progressively. The infant expired, and at autopsy, dissection of the heart revealed a large tumor mass in the interventricular septum. Histologically, the mass showed the classic "spider cells," and a diagnosis of cardiac rhabdomyoma of childhood was established. (C) 2009 Elsevier Inc. All rights reserved.
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Univ Toronto, Gen Hosp, Princess Margaret Hosp, Hlth Network,Dept Pathol, Toronto, ON M5G 2C4, CanadaUniv Toronto, Gen Hosp, Princess Margaret Hosp, Hlth Network,Dept Pathol, Toronto, ON M5G 2C4, Canada
Butany, J
Nair, V
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Nair, V
Naseemuddin, A
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Naseemuddin, A
Nair, GM
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Nair, GM
Catton, C
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Catton, C
You, T
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Univ Toronto, Gen Hosp, Princess Margaret Hosp, Hlth Network,Dept Pathol, Toronto, ON M5G 2C4, CanadaUniv Toronto, Gen Hosp, Princess Margaret Hosp, Hlth Network,Dept Pathol, Toronto, ON M5G 2C4, Canada
Butany, J
Nair, V
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Nair, V
Naseemuddin, A
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Naseemuddin, A
Nair, GM
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Nair, GM
Catton, C
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Catton, C
You, T
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