Faliure of bone morphogenetic protein receptor trafficking in pulmonary arterial hypertension: Potential for rescue?

被引:0
作者
Sobolewski, A. [1 ]
Rudarakanchana, N. [1 ]
Jeffery, T. K. [1 ]
Trembath, R. C. [1 ]
Morrell, N. W. [1 ]
机构
[1] Univ Cambridge, Sch Clin Med, Dept Med, Cambridge, England
关键词
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:II11 / II11
页数:1
相关论文
共 50 条
  • [31] CATHEPSIN L CONTRIBUTES TO THE DEVELOPMENT OF PULMONARY ARTERIAL HYPERTENSION VIA DEGRADATION OF BONE MORPHOGENETIC PROTEIN TYPE II RECEPTOR
    Peng, Zhouyf
    JOURNAL OF HYPERTENSION, 2018, 36 : E59 - E59
  • [32] Bone Morphogenetic Protein Receptor Type II and Inflammation Are Bringing Old Concepts into the New Pulmonary Arterial Hypertension World
    Perros, Frederic
    Bonnet, Sebastien
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2015, 192 (07) : 777 - 779
  • [33] Bone Morphogenic Protein Type 2 Receptor Mutation-Independent Mechanisms of Disrupted Bone Morphogenetic Protein Signaling in Idiopathic Pulmonary Arterial Hypertension
    Barnes, Jarrod W.
    Kucera, Elif T.
    Tian, Liping
    Mellor, Noel E.
    Dvorina, Nina
    Baldwin, William W., III
    Aldred, Micheala A.
    Farver, Carol F.
    Comhair, Suzy A. A.
    Aytekin, Metin
    Dweik, Raed A.
    AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY, 2016, 55 (04) : 564 - 575
  • [34] Increased Bone Morphogenetic Protein 10 in Pulmonary Hypertension
    Llucia-Valldeperas, Aida
    Van Wezenbeek, Jessie
    Groeneveldt, Joanne
    Smal, Rowan
    Sanchez-Duffhues, Gonzalo
    Becher, Clarissa
    Noordegraaf, Anton Vonk
    Bogaard, Harm J.
    Goumans, Marie Jose
    De Man, Frances S.
    CIRCULATION, 2022, 146
  • [35] Elevated Levels of Circulating Bone Morphogenetic Protein 7 Predict Mortality in Pulmonary Arterial Hypertension
    Liu, Dong
    Wu, Bing-Xiang
    Sun, Na
    Yan, Yi
    Yuan, Ping
    Qu, Jie-Ming
    Jing, Zhi-Cheng
    CHEST, 2016, 150 (02) : 367 - 373
  • [36] BONE MORPHOGENETIC PROTEIN RECEPTOR-II REGULATES PULMONARY ARTERY ENDOTHELIAL CELL BARRIER FUNCTION: RELEVANCE TO HERITABLE PULMONARY ARTERIAL HYPERTENSION
    Burton, V. J.
    Ciuclan, L. I.
    Holmes, A. M.
    Rodman, D.
    Walker, C.
    Budd, D. C.
    THORAX, 2010, 65 : A69 - A69
  • [37] Bone Morphogenetic Protein Receptor 2 Mutations Impair T Regulatory Cell Function and Promote Inflammation in Pulmonary Arterial Hypertension
    Peng, G.
    Tian, A.
    Guan, T.
    Wu, T.
    Nicolls, M. R.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2020, 201
  • [38] Sildenafil Potentiates Bone Morphogenetic Protein Signaling in Pulmonary Arterial Smooth Muscle Cells and in Experimental Pulmonary Hypertension
    Yang, Jun
    Li, Xiaohui
    Al-Lamki, Rafia S.
    Wu, Changxin
    Weiss, Astrid
    Berk, Joachim
    Schermuly, Ralph T.
    Morrell, Nicholas W.
    ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY, 2013, 33 (01) : 34 - +
  • [39] Modulation of Endothelial Bone Morphogenetic Protein Receptor Type 2 Activity by Vascular Endothelial Growth Factor Receptor 3 in Pulmonary Arterial Hypertension
    Hwangbo, Cheol
    Lee, Heon-Woo
    Kang, Hyeseon
    Ju, Hyekyung
    Wiley, David S.
    Papangeli, Irinna
    Han, Jinah
    Kim, Jun-Dae
    Dunworth, William P.
    Hu, Xiaoyue
    Lee, Seyoung
    El-Hely, Omar
    Sofer, Avraham
    Pak, Boryeong
    Peterson, Laura
    Comhair, Suzy
    Hwang, Eun Mi
    Park, Jae-Yong
    Thomas, Jean-Leon
    Bautch, Victoria L.
    Erzurum, Serpil C.
    Chun, Hyung J.
    Jin, Suk-Won
    CIRCULATION, 2017, 135 (23) : 2288 - +
  • [40] Intrinsic Bone Morphogenetic Protein Antagonist Gremlin 1 as a Potential Biomarker for Therapy Efficacy in a Rat Model of Pulmonary Arterial Hypertension
    Cantoni, S.
    Pastore, F.
    Schiavi, E.
    Cont, M.
    Pareti, S.
    Facchinetti, F.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2023, 207