Successful Surgical Pulmonary Artery Reconstruction in Arterial Tortuosity Syndrome

被引：9

作者：

Al-Khaldi, Abdulaziz ^{[1
]}

Alharbi, Abdulmohsen

Tamimi, Omar

Mohammed, Yasser

机构：

[1] King Abdul Aziz Med City, Div Cardiac Surg, Riyadh 11426, Saudi Arabia

来源：

ANNALS OF THORACIC SURGERY | 2009年 / 88卷 / 04期

关键词：

CHROMOSOME; 20Q13; HOMOZYGOSITY; VESSELS;

D O I：

10.1016/j.athoracsur.2009.02.020

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The outcomes of surgical repair for diffuse pulmonary artery stenoses due to arterial tortuosity syndrome are unknown. We report a 1-year-old girl with tortuosity syndrome who presented with suprasystemic right ventricular pressure due to distortion and stenoses of the pulmonary artery branches. We describe the operative findings of this unique pathology and the surgical techniques used to completely reconstruct the pulmonary arterial tree, with normalization of the right ventricular pressure. (Ann Thorac Surg 2009; 88: 1343-5) (C) 2009 by The Society of Thoracic Surgeons

引用

页码：1343 / 1345

页数：4

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