Fatal outcome of sleep apnoea in PWS during the initial phase of growth hormone treatment - A case report

被引：46

作者：

Eiholzer, U ^{[1
]}

Nordmann, Y ^{[1
]}

l'Allemand, D ^{[1
]}

机构：

[1] Fdn Growth Puberty Adolescence, CH-8006 Zurich, Switzerland

来源：

HORMONE RESEARCH | 2002年 / 58卷

关键词：

Prader-Willi syndrome; respirational abnormalities; hypoventilation; sudden death;

D O I：

10.1159/000066478

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The case of a boy with Prader-Willi syndrome (PWS) who suffered from respiratory problems since birth and suddenly died at the age of 6.5 years, 4 months after initiation of GH therapy, is presented. This case indicates the possibility of fatal courses in infants and children with PWS as a consequence of respiratory problems and raises the question as to a causal connection between the initiation of GH therapy and the sudden death of this child. Copyright (C) 2002 S. Karger AG, Basel.

引用

页码：24 / 26

页数：3

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