Modified Norwood operation for the newborn with hypoplastic left heart syndrome and Turner syndrome. A report of successful surgical treatment

被引:0
作者
Wojcik, Elzbieta [1 ]
Skalski, Janusz H. [1 ]
Mroczek, Tomasz [1 ]
Kolcz, Jacek [1 ]
Dudynska, Miroslawa [1 ]
Jarosz, Jerzy [1 ]
Kordon, Zbigniew [2 ]
Rudzinski, Andrzej [2 ]
机构
[1] Wydzial Lekarski UJ Coll Med, Polsko Amer Inst Pediat, Klin Kardiochirurg Dzieciecej UJ Coll Med, Krakow, Poland
[2] Wydzial Lekarski UJ Coll Med, Polsko Amer Inst Pediat, Klin Kardiol Dzieciecej UJ Coll Med, Krakow, Poland
来源
KARDIOCHIRURGIA I TORAKOCHIRURGIA POLSKA | 2009年 / 6卷 / 02期
关键词
paediatric cardiac surgery; congenital heart defects; hypoplastic left heart syndrome; Turner syndrome; Norwood operation; RIGHT VENTRICLE; MALFORMATIONS; PALLIATION;
D O I
暂无
中图分类号
R61 [外科手术学];
学科分类号
摘要
Hypoplastic left heart syndrome (HLHS) is a complex cyanotic congenital heart defect with wide anatomical variability. HLHS requires multi-stage operative treatment according to the Fontan principle for single ventricle CHD. The first stage of treatment is Norwood operation performed in newborn age. Coexistence of genetic syndromes, including Turner syndrome, is an independent risk factor for the first stage of HLHS treatment by Norwood operation. The report presents the course of a successful treatment of the first stage with the modified Norwood operation of a newborn with prenatal diagnosis of Turner syndrome and CHD of type HLHS.
引用
收藏
页码:135 / 137
页数:3
相关论文
共 10 条
[1]  
Bondy Carolyn A, 2008, Congenit Heart Dis, V3, P2, DOI 10.1111/j.1747-0803.2007.00163.x
[2]   Turner syndrome and clinical treatment [J].
Hjerrild, Britta E. ;
Mortensen, Kristian Havmand ;
Gravholt, Claus H. .
BRITISH MEDICAL BULLETIN, 2008, 86 (01) :77-93
[3]   Management of 239 patients with hypoplastic left heart syndrome and related malformations from 1993 to 2007 [J].
Jacobs, Jeffrey P. ;
O'Brien, Sean M. ;
Chai, Paul J. ;
Morell, Victor O. ;
Lindberg, Harald L. ;
Quintessenza, James A. .
ANNALS OF THORACIC SURGERY, 2008, 85 (05) :1691-1697
[4]   Right ventricle to pulmonary artery conduit reduces interim mortality after stage 1 Norwood for hypoplastic left heart syndrome [J].
Pizarro, C ;
Mroczek, T ;
Malec, E ;
Norwood, WI .
ANNALS OF THORACIC SURGERY, 2004, 78 (06) :1959-1963
[5]   Stage I palliation for hypoplastic left heart syndrome: Norwood versus Sano modification [J].
Reemtsen, Brian L. ;
Pike, Nancy A. ;
Starnes, Vaughn A. .
CURRENT OPINION IN CARDIOLOGY, 2007, 22 (02) :60-65
[6]   Outcome of infants with hypoplastic left heart and Turner syndromes [J].
Reis, PM ;
Punch, MR ;
Bove, EL ;
Van de Ven, CJM .
OBSTETRICS AND GYNECOLOGY, 1999, 93 (04) :532-535
[7]   Right ventricle-pulmonary artery shunt in first-stage palliation of hypoplastic left heart syndrome [J].
Sano, S ;
Ishino, K ;
Kawada, M ;
Arai, S ;
Kasahara, S ;
Asai, T ;
Masuda, Z ;
Takeuchi, M ;
Ohtsuki, S .
JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, 2003, 126 (02) :504-510
[8]   Turner's syndrome in fetal life [J].
Surerus, E ;
Huggon, IC ;
Allan, LD .
ULTRASOUND IN OBSTETRICS & GYNECOLOGY, 2003, 22 (03) :264-267
[9]   Cardiovascular malformations and complications in Turner syndrome [J].
Sybert, VP .
PEDIATRICS, 1998, 101 (01) :E11
[10]  
VANEGMOND H, 1988, BRIT HEART J, V60, P69