Lymphocytic interstitial pneumonia associated with common variable immunodeficiency resolved with intravenous immunoglobulins

被引:22
作者
Arish, N.
Eldor, R.
Fellig, Y.
Bogot, N.
Laxer, U.
Izhar, U.
Rokach, A.
机构
[1] Hebrew Univ Jerusalem, Hadassah Med Ctr, Inst Pulmonol, IL-91120 Jerusalem, Israel
[2] Hebrew Univ Jerusalem, Hadassah Med Ctr, Dept Med C, IL-91120 Jerusalem, Israel
[3] Hebrew Univ Jerusalem, Hadassah Med Ctr, Dept Pathol, IL-91120 Jerusalem, Israel
[4] Hebrew Univ Jerusalem, Hadassah Med Ctr, Inst Radiol, IL-91120 Jerusalem, Israel
[5] Hebrew Univ Jerusalem, Hadassah Med Ctr, Dept Cardiothorac Surg, IL-91120 Jerusalem, Israel
关键词
D O I
10.1136/thx.2004.029819
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Lymphocytic interstitial pneumonia ( LIP) is a rare form of interstitial lung disease. A few case reports have described an association with common variable immunodeficiency (CVID). Corticosteroids are usually used to treat symptomatic patients but their efficacy has never been studied in a controlled trial. We describe a patient with LIP and CVID who was treated monthly with intravenous immunoglobulins ( IVIG) without steroids. The patient improved dramatically. We believe that, in selected cases of LIP and immunodeficiency, IVIG given monthly should be considered as the only treatment without adding steroids.
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收藏
页码:1096 / 1097
页数:2
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