Adult cellular rhabdomyoma of the heart: A report of 3 cases

被引:8
作者
Burke, AP
Gatto-Weis, C
Griego, JE
Ellington, KS
Virmani, R [1 ]
机构
[1] Armed Forces Inst Pathol, Dept Cardiovasc Pathol, Washington, DC 20306 USA
[2] Med Coll Penn & Hahnemann Univ, Dept Pathol & Lab Med, Hahnemann Univ Hosp, Philadelphia, PA 19129 USA
[3] Presbyterian Hosp, Dept Pathol, Albuquerque, NM USA
[4] Duke Univ, Med Ctr, Durham, NC USA
关键词
hamartoma; heart; myogenin; neoplasm; rhabdomyoma;
D O I
10.1053/hupa.2002.129418
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
We present 3 adults with cardiac rhabdomyomas, 2 in the atria and 1 in the right ventricle. One atrial tumor was discovered incidentally, and 1 resulted in supraventricular tachyeardia. The ventricular lesion caused ventricular tachycardia. Compared with congenital rhabdomyomas, the tumors are relatively cellular, the cells are smaller, there are few spider cells, and there is evidence of cell proliferation. Two of the 3 tumors demonstrated spindling in contrast to adult rhabdomyomas of the head and neck. Although surgical excision was possible in all patients, long-term follow-up will be required to determine the true biologic behavior of these neoplasms. HUM PATHOL 33: 1092-1097. Copyright 2002, Elsevier Science (USA). All rights reserved.
引用
收藏
页码:1092 / 1097
页数:6
相关论文
共 13 条
[1]  
BURKE AP, 1991, MODERN PATHOL, V4, P70
[2]   Hamartoma of mature cardiac myocytes [J].
Burke, AP ;
Ribe, JK ;
Bajaj, AK ;
Edwards, WD ;
Farb, A ;
Virmani, R .
HUMAN PATHOLOGY, 1998, 29 (09) :904-909
[3]   Are myogenin and MyoD1 expression specific for rhabdomyosarcoma? A study of 150 cases, with emphasis on spindle cell mimics [J].
Cessna, MH ;
Zhou, H ;
Perkins, SL ;
Tripp, SR ;
Layfield, L ;
Daines, C ;
Coffin, CM .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 2001, 25 (09) :1150-1157
[4]   TUBEROUS SCLEROSIS - AN UNUSUAL CAUSE OF SEIZURES IN AN 18 YEAR-OLD [J].
DESILVA, DC ;
JOHNSTON, AW ;
DEAN, JCS .
SCOTTISH MEDICAL JOURNAL, 1994, 39 (01) :19-20
[5]   ECHOCARDIOGRAPHIC DIAGNOSIS OF CARDIAC TUMORS IN SYMPTOMATIC TUBEROUS SCLEROSIS PATIENTS [J].
DIAMANT, S ;
SHARAZ, J ;
HOLTZMAN, M ;
LANIADO, S .
CLINICAL PEDIATRICS, 1983, 22 (04) :297-299
[6]   CARDIAC RHABDOMYOMA - CLINICOPATHOLOGIC AND ELECTRON-MICROSCOPIC STUDY [J].
FENOGLIO, JJ ;
MCALLISTER, HA ;
FERRANS, VJ .
AMERICAN JOURNAL OF CARDIOLOGY, 1976, 38 (02) :241-251
[7]  
GERDES J, 1984, J IMMUNOL, V133, P1710
[8]   Significance of myocytes with positive DNA in situ nick end-labeling (TUNEL) in hearts with dilated cardiomyopathy - Not apoptosis but DNA repair [J].
Kanoh, M ;
Takemura, G ;
Misao, J ;
Hayakawa, Y ;
Aoyama, T ;
Nishigaki, K ;
Noda, T ;
Fujiwara, T ;
Fukuda, K ;
Minatoguchi, S ;
Fujiwara, H .
CIRCULATION, 1999, 99 (21) :2757-2764
[9]   ADULT RHABDOMYOMA OF THE HEAD AND NECK - A CLINICOPATHOLOGICAL AND IMMUNOPHENOTYPIC STUDY [J].
KAPADIA, SB ;
MEIS, JM ;
FRISMAN, DM ;
ELLIS, GL ;
HEFFNER, DK ;
HYAMS, VJ .
HUMAN PATHOLOGY, 1993, 24 (06) :608-617
[10]   FETAL RHABDOMYOMA OF THE HEAD AND NECK - A CLINICOPATHOLOGICAL AND IMMUNOPHENOTYPIC STUDY OF 24 CASES [J].
KAPADIA, SB ;
MEIS, JM ;
FRISMAN, DM ;
ELLIS, GL ;
HEFFNER, DK .
HUMAN PATHOLOGY, 1993, 24 (07) :754-765