Haemangioblastomas: clinical, epidemiological and pathological findings in 14 cases

被引:4
作者
Gasparetto, EL [1 ]
Faoro, LN [1 ]
Filho, JSR [1 ]
Torres, LFB [1 ]
机构
[1] UFPR, Hosp Clin, Serv Anat Patol, Secao Microscopia Eletron & Neuropatol, BR-80060900 Curitiba, Parana, Brazil
关键词
haemangioblastoma; central nervous system; tumours; phacomatosis;
D O I
10.1590/S0004-282X2000000200018
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
We report the clinical, epidemiological and pathological findings of 14 patients with haemangioblastoma. Sixty-four percent occurred in males, with ages ranging from 16 to 60 years, with an average of 34,4 years. Most of the tumours were confined to the cerebellum (n=9). The most frequent symptoms were headache (n=7) and dizziness (n=7), with a mean duration of 70 days. Von Hippel-Lindau syndrome (vHL) was diagnosed in 3 patients. Eleven patients were submitted to total surgical removal and in 3 the tumour was partially ressected. A relapse rate of 28% in 3 years of follow-up was found. The patients with vHL showed recurrence in 66% of the cases. These findings corroborate those in current medical literature, showing an increased morbidity of this tumor when associated with vHL.
引用
收藏
页码:310 / 314
页数:5
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