A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin

被引：1

作者：

Sciume, Mariarita ^{[1
]}

Serpenti, Fabio ^{[2
]}

Muratori, Simona ^{[3
]}

Pravettoni, Valerio ^{[4
]}

Ulivieri, Fabio Massimo ^{[5
]}

Croci, Giorgio Alberto ^{[6
]}

Migliorini, Anna Chiara ^{[7
]}

Esposito, Andrea ^{[8
]}

Goldaniga, Maria Cecilia ^{[1
]}

Saporiti, Giorgia Natascia ^{[1
]}

Galassi, Giulia ^{[1
]}

Baldini, Luca ^{[1
,2
]}

Onida, Francesco ^{[1
,2
]}

Grifoni, Federica Irene ^{[1
]}

机构：

[1] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Hematol Unit, Milan, Italy

[2] Univ Milan, Milan, Italy

[3] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Dept Physiopathol & Transplantat, Dermatol Unit, Milan, Italy

[4] Fdn IRCCS Ca Granda Osped Maggiore Policlin, UOC Gen Med Immunol & Allergol, Milan, Italy

[5] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Bone Metab Unit, Nucl Med, Milan, Italy

[6] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Dept Pathophysiol & Transplantat, Div Pathol, Milan, Italy

[7] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Serv Immunoematol & Trasfus, Lab Ematol, Milan, Italy

[8] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Div Radiol, Milan, Italy

来源：

CLINICAL CASE REPORTS | 2021年 / 9卷 / 02期

关键词：

bulky lymphadenopathy; midostaurin; purine analogue; systemic mastocytosis; ADULTS; NEOPLASMS; EFFICACY; SAFETY;

D O I：

10.1002/ccr3.3717

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.

引用

页码：978 / 982

页数：5

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