Neuro-Behcet disease with predominant involvement of the brainstem

被引:18
作者
Mirsattari, SM
McGinn, GJ
Halliday, WC
机构
[1] Univ Western Ontario, London Hlth Sci Ctr, Dept Clin Neurol Sci, London, ON N6A 5A5, Canada
[2] Univ Manitoba, Dept Radiol, Winnipeg, MB, Canada
[3] Univ Toronto, Dept Pathol, Toronto, ON, Canada
关键词
D O I
10.1212/01.WNL.0000130192.12100.8D
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a patient with relapsing-remitting meningoencephalitis secondary to neuro-Behcet disease which resulted in recurrent brainstem encephalitis. MRI revealed increased signal intensity on the proton density and T2-weighted images and gadolinium enhancement during relapses. Autopsy revealed acute on chronic meningoencephalomyelitis involving the entire CNS, which was most marked in the brainstem.
引用
收藏
页码:382 / 384
页数:3
相关论文
共 10 条
  • [1] Hadfield MG, 1997, CLIN NEUROPATHOL, V16, P55
  • [2] PRIMARY STRUCTURE OF A HUMAN MITOCHONDRIAL PROTEIN HOMOLOGOUS TO THE BACTERIAL AND PLANT CHAPERONINS AND TO THE 65-KILODALTON MYCOBACTERIAL ANTIGEN
    JINDAL, S
    DUDANI, AK
    SINGH, B
    HARLEY, CB
    GUPTA, RS
    [J]. MOLECULAR AND CELLULAR BIOLOGY, 1989, 9 (05) : 2279 - 2283
  • [3] KAHAN A, 1992, J RHEUMATOL, V19, P741
  • [4] ASSOCIATION BETWEEN THE 65-KILODALTON HEAT-SHOCK PROTEIN, STREPTOCOCCUS-SANGUIS, AND THE CORRESPONDING ANTIBODIES IN BEHCETS-SYNDROME
    LEHNER, T
    LAVERY, E
    SMITH, R
    VANDERZEE, R
    MIZUSHIMA, Y
    SHINNICK, T
    [J]. INFECTION AND IMMUNITY, 1991, 59 (04) : 1434 - 1441
  • [5] PERVIN K, 1993, J IMMUNOL, V151, P2273
  • [6] MENINGO-ENCEPHALITIS OF BEHCETS DISEASE - CASE REPORT WITH PATHOLOGICAL FINDINGS
    RUBINSTEIN, LJ
    URICH, H
    [J]. BRAIN, 1963, 86 (01) : 151 - &
  • [7] Current concepts - Behcet's disease
    Sakane, T
    Takeno, M
    Suzuki, N
    Inaba, G
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1999, 341 (17) : 1284 - 1291
  • [8] SILMAN AJ, 1990, LANCET, V335, P1078
  • [9] BEHCETS-DISEASE
    STRATIGOS, AJ
    LASKARIS, G
    STRATIGOS, JD
    [J]. SEMINARS IN NEUROLOGY, 1992, 12 (04) : 346 - 357
  • [10] YOUNG C, 1988, CLIN EXP IMMUNOL, V73, P6