Congenital cutaneous multifocal kaposiform hemangioendothelioma

被引:31
作者
Gianotti, R [1 ]
Gelmetti, C [1 ]
Alessi, E [1 ]
机构
[1] Univ Milan, Ist Sci Dermatol, IRCCS, Osped Maggiore, I-20122 Milan, Italy
关键词
vascular neoplasms; congenital vascular neoplasms; children;
D O I
10.1097/00000372-199912000-00010
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Kaposiform hemangioendothelioma is a rare vascular neoplasm in children often associated with Kasabach-Merritt syndrome. The tumor usually presents in retroperitoneal location and is rarely present at birth. Cutaneous lesions manifest after birth and must be clinically differentiated from infantile hemangiomas and diffuse neonatal hemangiomatosis. Histologically, it bears similarities with Kaposi sarcoma. We present a case of congenital cutaneous multifocal kaposiform hemangioendothelioma (KHE).
引用
收藏
页码:557 / 561
页数:5
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