Uterine perivascular epithelioid cell neoplasms (PEComas): report of two cases and literature review

被引：0

作者：

Cossu, A. ^{[1
]}

Paliogiannis, P. ^{[1
]}

Tanda, F. ^{[1
]}

Dessole, M. ^{[2
]}

Dessole, S. ^{[2
]}

Palmieri, G. ^{[3
]}

Capobianco, G. ^{[2
]}

机构：

[1] Univ Sassari, Dept Surg Microsurg & Med Sci, I-07100 Sassari, Italy

[2] Univ Sassari, Dept Surg Microsurg & Med Sci, Gynecol & Obstet Clin, I-07100 Sassari, Italy

[3] CNR, Inst Biomol Chem, Canc Genet Unit, Sassari, Italy

来源：

EUROPEAN JOURNAL OF GYNAECOLOGICAL ONCOLOGY | 2014年 / 35卷 / 03期

关键词：

Perivascular epithelioid cell tumors (PEComas); Uterus; Histology; Review; TUMOR; ORIGIN;

D O I：

暂无

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Perivascular epithelioid cell tumors (PEComas) are rare tumors characterized by co-expression of melanocytic and smooth muscle markers. PEComas have been reported in a wide variety of anatomic sites. In the female genital tract, PEComas most frequently affect the uterus. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS). PEComas have an unpredictable biologic behavior, with some tumors being unresectable or metastatic at the time of diagnosis. The risk of aggressive behavior of these tumors has been linked to a number of factors evaluable on histopathological review following initial surgical resection. The authors report two cases of PEComa-NOS of the uterus: one with disease confined to uterus and the other case with lung and liver metastasis.

引用

页码：309 / 312

页数：4

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