Objectives: To report a rare case of moyamoya syndrome with primary antiphospholipid syndrome (APS). Clinical Presentation and Intervention: A 41-year-old woman was admitted with sudden onset of left-sided hemiparesis. Magnetic resonance imaging and magnetic resonance angiography of the brain showed characteristic features of moyamoya vessels. Laboratory investigations revealed raised levels of anticardiolipin antibody. She made a complete and uneventful recovery with aspirin and intensive physiotherapy over a period of 2 weeks. Conclusion: The association of APS and moyamoya disease may present a dilemma in management. While APS is often considered to be an indication for giving anticoagulation, a trial of antiplatelet agents is preferable to anticoagulation because of the risk of bleeding from the fragile moyamoya vessels. Copyright (C) 2006 S. Karger AG, Basel.
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Univ Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, BrazilUniv Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, Brazil
Kuhl Torricelli, A.
Remiao Ugolini-Lopes, M.
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Univ Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, BrazilUniv Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, Brazil
Remiao Ugolini-Lopes, M.
Bonfa, E.
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Univ Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, BrazilUniv Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, Brazil
Bonfa, E.
Andrade, D.
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Univ Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, BrazilUniv Sao Paulo FMUSP, Rheumatol Div, Fac Med, Hosp Clin HCFMUSP, Sao Paulo, Brazil
机构:
Hosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
Yamakami, L. Y. S.
Serafini, P. C.
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Hosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
Serafini, P. C.
de Araujo, D. B.
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Hosp Serv Publ Estadual Sao Paulo, Div Rheumatol, Sao Paulo, Brazil
Hosp Serv Publ Estadual Sao Paulo, Dept Rheumatol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
de Araujo, D. B.
Bonfa, E.
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Hosp Serv Publ Estadual Sao Paulo, Div Rheumatol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
Bonfa, E.
Leon, E. P.
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Hosp Serv Publ Estadual Sao Paulo, Div Rheumatol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
Leon, E. P.
Baracat, E. C.
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Hosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil
Baracat, E. C.
Silva, C. A.
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Hosp Serv Publ Estadual Sao Paulo, Div Rheumatol, Sao Paulo, Brazil
Univ Sao Paulo, Fac Med, Pediat Rheumatol Unit, Sao Paulo, BrazilHosp Serv Publ Estadual Sao Paulo, Dept Gynecol, Sao Paulo, Brazil