Autonomic failure is rare in patients with Sjogren syndrome (SS). We report the case of a 46-year-old woman with severe autonomic cardiovascular failure, manifested by incapacitating postural hypotension, as the first symptom of primary SS. Treatment with glucocorticoid resulted in a dramatic improvement of her symptoms and objective findings of autonomic cardiovascular dysfunction. We suggest that SS should be considered in patients with idiopathic autonomic cardiovascular neuropathy, especially in those with idiopathic orthostatic hypotension. Furthermore, glucocorticoid therapy seems to be very efficacious in the treatment of SS-associated autonomic cardiovascular neuropathy.
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Sri Ramachandra Inst Higher Educ & Res Deemed Univ, Chennai, Tamil Nadu, IndiaSri Ramachandra Inst Higher Educ & Res Deemed Univ, Chennai, Tamil Nadu, India
Kataria, Riya
Suja, Lakshmanan
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Sri Ramachandra Univ Med Coll, Gen Med, Chennai, Tamil Nadu, IndiaSri Ramachandra Inst Higher Educ & Res Deemed Univ, Chennai, Tamil Nadu, India
Suja, Lakshmanan
Anil, Archa Anna
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Sri Ramachandra Inst Higher Educ & Res, Gen Med, Chennai, Tamil Nadu, IndiaSri Ramachandra Inst Higher Educ & Res Deemed Univ, Chennai, Tamil Nadu, India
Anil, Archa Anna
Senthil, Narayanasamy
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Sri Ramachandra Inst Higher Educ & Res, Gen Med, Chennai, Tamil Nadu, IndiaSri Ramachandra Inst Higher Educ & Res Deemed Univ, Chennai, Tamil Nadu, India
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Yamashita, Hiroyuki
Eri, Toshiki
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Eri, Toshiki
Ueda, Yo
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Ueda, Yo
Ozaki, Takashi
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Ozaki, Takashi
Takahashi, Hiroyuki
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Takahashi, Hiroyuki
Tsuno, Takahiro
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Tsuno, Takahiro
Takahashi, Yuko
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Takahashi, Yuko
Kano, Toshikazu
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan
Kano, Toshikazu
Mimori, Akio
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Natl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Div Rheumat Dis, Shinju Ku, Tokyo 1628655, Japan